No abstract available.
Embryonic Stem Cells ; Neural Crest

Ganglioneuroma is a rare benign tumor which originates in the neural crest, and is found along the path of the sympathetic chain, from the base of the skull to the pelvic cavity. Due to the slow growth of this type of tumor, it may be detected incidentally, or detected by virtue of the attendant pressure effects on adjacent structures. We report one case of ganglioneuroma arising in the pelvic cavity.
Ganglioneuroma ; Neural Crest ; Skull ; Virtues

Pheochromocytoma, derived from the neural crest, is one of the surgically curable hypertensive syndromes The clinical manifestations in patients with pheochromocytoma are highly variable. The vast majority are functioning tumors but approximately 10 per cent of patients with pheochromocytoma are asymptomatic. Pheochromocytoma is a highly vascular tumor and not infrequently undergoes hemorrhagic necrosis and pseudocyst formation. Herein we report a case of nonfunctioning cystic pheochromocytoma in 32-year-old man.
Adult ; Humans ; Necrosis ; Neural Crest ; Pheochromocytoma*

Lipomatous neurofibroma is a recently described, very rare variant of neurofibroma. It shows a well-circumscribed nodule consisting of fascicles or whorls of spindle cells with an extensive lipomatous component. These fat cells are considered to be an integral part of this tumor, not a metaplastic or degenerative process. It may be due to the differentiation of local stem cells of neural crest. Herein we report a case of lipomatous neurofibroma, the rare pathological variant of neurofibroma with extensive mature fat cells.
Adipocytes ; Neural Crest ; Neurofibroma ; Stem Cells

Exraadrenal paragangliomas are rare tumors of a neural crest origin. Their preoperative diagnosis can be suspected from the clinical history and biochemical examination of the catecholamines or their metabolic by-products. Surgery is the mainstay of therapy, but surgical removal makes an additional problem for the repair of the ureteral defect if a paraganglioma is located near the ureter or if it encloses the ureter. The ureteral repair often poses a therapeutic dilemma, and especially when the ureteral defect is too extensive to be repaired with traditional methods. We report here on a case of successful replacement with using appendix for the repair of a long ureteral defect that was caused by a retroperitoneal paraganglioma.
Appendix* ; Catecholamines ; Diagnosis ; Neural Crest ; Paraganglioma* ; Ureter*

Ganglioneuroma is a rare benign tumor originating from the neural crest cells. It occurs most commonly in the retroperitoneum and posterior mediastinum and is often found in the neck or pelvis. It may be detected incidentally or detected by pressure effects on the adjacent structures due to its slow growth. However, some functional tumors may secrete catecholamines and present with some clinical symptoms. Complete surgical excision is the treatment of choice. We describe here a case of a retroperitoneal ganglioneuroma which was removed completely by surgery. We review the literature and discuss the clinical features of a ganglioneuroma.
Catecholamines ; Ganglioneuroma ; Mediastinum ; Neck ; Neural Crest ; Pelvis

Neural crest cells have embriologically important role for the development and growth in oral and maxillofacial region. If the early hereditary defect occurs or environmental factors affect these cells diminutive mesenchymal cells are disabled to make neural plate and decreased proliferation of mesenchymal cells result in hypoplastic development of neural crest. As a result, this brings about severe facial malformations such as various located facial clefts and/or loss or duplication of facial structure. These are two cases of accessory maxilla and zygomatic deformity with and without facial cleft.
Congenital Abnormalities ; Growth and Development ; Maxilla* ; Neural Crest ; Neural Plate

Ganglioneuroma is the most differentiated tumor of neural crest origin and rarely arises in the adrenal gland. Ganglioneuroma is typically known to be benign, but very rarely can metastasize to distant sites. We report a case of a 31-year-old man with a huge adrenal mass with hepatic metastases.
Adrenal Glands ; Adult ; Ganglioneuroma ; Humans ; Neoplasm Metastasis ; Neural Crest

Ganglioneuromas of retroperitoneal cavity which not originate from adrenal gland are very rare tumor, and usually recognized incidental to some other aliment or on a routine physical examination. Ganglioneuromas are generally considered to be the mature form of a triad of tumors arising from neural crest tissue which include malignant neuroblastoma and ganglioneuroblastoma. We report one case of retroperitoneal non-adrenal ganglioneuroma with review of literature.
Adrenal Glands ; Ganglioneuroblastoma ; Ganglioneuroma* ; Neural Crest ; Neuroblastoma ; Physical Examination

Pheochromocytoma, derived from the neural crest, accounts for less than one percent of all patients with hypertension, but is most important because of its potentially lethal nature. It may occur at any age, and surgeons are often first to see the disease because of sudden hypertensive crises during anesthesia or unexplained shock following operations. Herein we report a case of right adrenal pheochromocytoma in 57-yr-old woman who was successfully treated with surgical intervention.
Anesthesia ; Female ; Humans ; Hypertension ; Neural Crest ; Pheochromocytoma* ; Shock