Among the connective tissue diseases,Behcet's disease (BD)outrank systemic lupus erythematosus as a cause of venous occlusive disease.Deep vein thrombosis and superficial thrombophlebitis of the lower extremities are the most common venous lesions found in BD.We report a rare case of superficial venous thrombosis and thrombophlebitis of the abdomen,which was misdiagnosed as superficial mass in a previously undiagnosed BD patient.
Abdomen* ; Connective Tissue ; Humans ; Lower Extremity ; Lupus Erythematosus, Systemic ; Thrombophlebitis* ; Thrombosis* ; Veins ; Venous Thrombosis

A 17-year-old man was referred to our hospital because of dizziness and mild dyspnea. He had a history of partial thyroidectomy due to benign mass when he was 10 year-old. His conjunctiva was anemic and acral keratosis was noted. He had a goiter and a previous surgical scar on the anterior neck just below the thyroid cartilage. Blood counts were as follows; Hb was 4.3 g/dL, WBC 5,500/mm3, PLT 366,000/ mm3. Esophagogastroduodenoscopy and colonoscopy showed esophageal acanthosis and numerous variable sized polyps in the stomach, duodenum and colon. The small bowel series showed numerous polypoid lesions in the entire small bowel. Gastric polyps revealed hamartoma and colon polyps revealed inflammatory polyp with lymphoid hyperplasia by pathologic examination. Thyroid ultrasonograph showed multiple nodules and cysts and I131 scintigraphy showed multiple cold and hot nodules in his remnant thyroid gland. We diagnosed the patient as Cowden's syndrome.
Adolescent ; Child ; Cicatrix ; Colon ; Colonoscopy ; Conjunctiva ; Dizziness ; Duodenum ; Dyspnea ; Endoscopy, Digestive System ; Goiter ; Hamartoma ; Hamartoma Syndrome, Multiple* ; Humans ; Hyperplasia ; Keratosis ; Neck ; Polyps ; Radionuclide Imaging ; Stomach ; Thyroid Cartilage ; Thyroid Gland ; Thyroid Nodule ; Thyroidectomy