No abstract available.
Brain ; Humans ; Myotonic Dystrophy

No abstract available.
Humans ; Myotonia* ; Myotonic Dystrophy*

No abstract available.
Hydrocephalus, Normal Pressure ; Myotonic Dystrophy

No abstract available.
Myotonic Dystrophy* ; Thoracic Surgery, Video-Assisted* ; Thymoma*

No abstract available.
Cesarean Section* ; Female ; Myotonic Dystrophy* ; Pregnancy

In patients with myotonic dystrophy (MD), impairment of the conduction system is a common and progressive finding. However, only a few cases of MD with cardiomyopathy have been reported. Herein we report a case of MD with progressive non-ischemic cardiomyopathy and severe electrocardiographic abnormalities.
Adult ; Cardiomyopathies ; Electrocardiography ; Humans ; Myotonic Dystrophy

No abstract available.
Cesarean Section ; Female ; Myotonic Dystrophy ; Pregnancy

Myotonia dystrophica or myotonia atrophica is inheritant disease which appears usually from 2nd or 3rd decade. This disorder is characterized by an impaired ability to relax a previously contracted muscle, muscle weakness and atrophy, cataract and multiple system involvement including the endocrines. The electrophysiological characteristics of myotonia dystrophica show a essential, differential features from the other myotonias with myopathic EMG changes. This paper describes 3 siblings with myotonia dystrophica and a case with no members of families clinically affected, and they were studied by clinically and by electromyographically.
Atrophy ; Cataract ; Humans ; Muscle Weakness ; Myotonia* ; Myotonic Dystrophy* ; Siblings

Myotonic dystrophy, a multi-systemic disease with cardiac involvement, is the most common inherited neuromuscular disease. Here, we report the results of radiofrequency catheter ablation of persistent atrial fibrillation in a patient with myotonic dystrophy and achalasia-like esophageal dilatation.
Atrial Fibrillation* ; Catheter Ablation* ; Dilatation* ; Humans ; Myotonic Dystrophy* ; Neuromuscular Diseases

Myotonia is characterized by failure of the voluntary muscles to relax immediately and persistence of contraction following voluntery movement or mechanical and electrical stimulation, Myotonic dystrophy (myotonia dystrophica, myotonia atrophica, Steinert's disease) is a hereditary progressive muscular abnormality with dominent transmittance and is characterized by myotonia, muscular wasting and weakness, and frequent association of frontal baldness, testicular atrophy, cataracts, and other nonmuscular abnormalities, We report a case of myotonic dystrophy in a 38 year-old man who had myotonia, muscular wasting and weakness, testicular atrophy, and frontal baldness, Electrodiagnostic studies indicated typical myotonic dystrophy. A review of literature is included.
Alopecia ; Atrophy ; Cataract ; Electric Stimulation ; Muscle, Skeletal ; Myotonia ; Myotonic Dystrophy