1.Soft tissue profile changes in micrognathia after distraction osteogenesis.
Xiao-Hui FU ; Jan CHEN ; Fei-Yun PING ; Feng-Guo YAN ; Yi-Dan SHAN
Chinese Journal of Plastic Surgery 2008;24(4):271-274
OBJECTIVETo evaluate the effect of distraction osteogenesis for severe micrognathia by comparing the pre- and post-operative profile and mentolabial relationship.
METHODS16 cases underwent temporal-mandibular joint plasty and temporal fasciomuscular flap transfer. The mandibular distraction began at the 5th postoperative day at a rate of 0.8 mm a day, two times a day. Bony and soft tissue cephalometry were performed before and after operation. T-test was used to study the change after distraction osteogenesis.
RESULTSThere were significant differences in facial convexity, lower facial height, lower lip length, inter-labial distance, the ratio of lip to mental, the distance from lip to esthetic plane, the depth of mentolabial crease and the thickness of mental soft tissue.
CONCLUSIONSMandibular distraction osteogenesis can markedly improve the soft tissue profile of the middle and lower face for severe micrognathia.
Child ; Child, Preschool ; Facial Muscles ; pathology ; Humans ; Male ; Micrognathism ; pathology ; surgery ; Osteogenesis, Distraction ; Postoperative Period
2.Hereditary Sclerosing Poikiloderma.
Hyo Jin LEE ; Dong Hoon SHIN ; Jong Soo CHOI ; Ki Hong KIM
Journal of Korean Medical Science 2012;27(2):225-227
Hereditary sclerosing poikiloderma (HSP) is a very rare disease. The clinical features are principally widespread poikiloderma and linear hyperkeratotic and sclerotic bands. We report an 18-yr-old male who presented reticular hyperpigmented lesions on the trunk and extremities since 2-yr-old. Also, linear sclerosing bands appeared on both antecubital and popliteal fossae after yr. Histopathologic finding showed dense sclerotic collagen fibers with telangiectasia in the upper dermis and fragmentations of damaged elastic fibers in the elastic stain, consistent with HSP. We report the first Korean case of HSP.
Abnormalities, Multiple
;
Adolescent
;
Elastic Tissue/pathology
;
Fingers/abnormalities
;
Humans
;
Hyperpigmentation/pathology
;
Male
;
Micrognathism/pathology
;
Rothmund-Thomson Syndrome/*diagnosis/pathology
;
Sclerosis/pathology
;
Skin Diseases/diagnosis/pathology