The authors experienced a case of secondary glaucoma combined with mesodermal dysgenesis of anterior segment, which disclosed extensive peripheral iridocorneal adhesion of congenital origin while his fellow eye revealed a sclerocornea. This case is extremely rare and entirely different from the previously reported Axenfeld's and Rieger's anomalies. We report this interesting case with brief review of the literatures.
Glaucoma* ; Mesoderm*

Persistent pupillary membrane ia a congenital anomaly which waa resulted from incomplete atrophy of the fetal vascular arcades and its associated mesodermal tissue derived from the primitive annular vessels. Authors experienced a case (female, 17 years old) of thick persistent pupillary membrane of both eyes which were required complete removal of these membranes under operating microscope. Her corrected vision has improved up to 0.5 (Rt. eye) from 0.1 and 0.7 (Lt eye) from 0.2 without diplopia after operation.
Atrophy ; Diplopia ; Membranes* ; Mesoderm

Primary tumors of the ureter are usually malignant and rare, a few are benign. Benign tumors arising from mesoderm are especially rare. But, recently the incidence rate was progressively increased due to developed methods of diagnostic procedures. We herein report a case of ureteral polyp in the left ureteropelvic junction with a brief review of literatures.
Incidence ; Mesoderm ; Polyps* ; Ureter*

Neurofibromatosis(von Reckling hausen's disease) is a congenital heredofamilial disorderresulting from dysplasia of neuroectodermal and mesodermal tissues. It is characterized by developmental anormaly, pigmentary skin lesions and multiple tumors derived from the Schwannian cells of the peripheral and sensory nerve. The authors have experienced two cases of Neurofibromatosis. which is clinically diagnosed. and confirmed by histopathological examination. It was reviewed clinically with the literature.
Mesoderm ; Neural Plate ; Neurofibromatoses* ; Skin

Congenital mesoblastic nephroma is a slow-growing tumor considered to originate from renal mesenchyme and usually discovered before the age of 6 months. The tumor is almost invariably benign but has been mistaken for Wilms` tumor and unnecessarily overtreated. We report a case of congenital mesoblastic nephroma in 2 months aged infant.
Humans ; Infant ; Mesoderm ; Nephroma, Mesoblastic*

Fibrous hamartoma of infancy (FHI) is a rare benign soft tissue tumor that is composed of an organoid pattern of fibrous tissue and primitive mesenchyme and adipose tissue. The majority of cases of fibrous hamartoma of infancy occur within the first year of life as a single painless subcutaneous nodule. We experienced and report on an uncommon case of protruding fibrous hamartoma of infancy in an 1-year-old girl.
Adipose Tissue ; Hamartoma ; Mesoderm ; Organoids

Fibrous hamartoma of infancy (FHI) is a rare benign soft tissue tumor that is composed of an organoid pattern of fibrous tissue and primitive mesenchyme and adipose tissue. The majority of cases of fibrous hamartoma of infancy occur within the first year of life as a single painless subcutaneous nodule. We experienced and report on an uncommon case of protruding fibrous hamartoma of infancy in an 1-year-old girl.
Adipose Tissue ; Hamartoma ; Mesoderm ; Organoids

Osteogenic sarcoma arise from primitive bone forming mesenchyme which is transformed into neoplastic osteoid and bone. Most osteogenic sarcomas originate in long bone, only rarely do they occur as primary tumor of the spine. A case is presented in which a patient who had suffered from paraplegia and self voiding difficulty. It was diagnosed as osteogenic sarcoma of the 5th thoracic spine which was operated and confirmed by microscopically, and is discussed with a brief review of the literatures.
Humans ; Mesoderm ; Osteosarcoma* ; Paraplegia* ; Spine*

Seminal vesicle cysts combined with ipsilateral renal agenesis represent a rare urologic anomaly. This urogenital malformation is explained as a developmental failure in the same mesodermal region. We report a case of seminal vesicle cyst, ipsilateral dilated ureter and renal agenesis which was treated by surgical excision. And we searched the literature to review the clinical presentation, diagnosis and treatment options of this anomaly.
Diagnosis ; Mesoderm ; Seminal Vesicles* ; Ureter*

Marfan syndrome is an uncommon congenital disease originally described by Marfan in 1896. It is inherited as an autosomal dominant trait and can affect the tissues of mesodermal origin, mainly skeletal, ocular, and cardio-vascular systems. We report 4 cases of Marfan syndrome occurring in one family, one of which was found to have an acute attack of glaucoma and underwent extract operation of a right dislocated lens. A brief summary of the literature is submitted.
Glaucoma ; Humans ; Marfan Syndrome ; Mesoderm