No abstract available.
Neurofibroma* ; Peripheral Nerves*

No abstract available.
Aged* ; Arm* ; Histiocytoma, Malignant Fibrous ; Humans

No abstract available.
Dermatitis*

Darier's disease is an uncommon genodermatosis, characterized by the symmetric eruption of keratotic papules, focal loss of epithelial adhesion and abnormal keratinization. A unilateral, or localized variant has been identified as a mosaic form, involving linear or 'zosteriform' epidermal lesions with clinical and histological features of Darier's disease. Some suggest that unilateral lesions should be classified as acantholytic dyskeratotic epidermal nevi, rather than localized Darier disease. A 17-year-old male presented with unilateral zosteriform distribution of brownish hyperkeratotic papules with ipsilateral v-notching of the thumb nail. A biopsy specimen revealed acantholysis, suprabasal cleft and multiple dyskeratotic cells. We report a case of unilateral Darier's disease which further supports unilateral dermatologic manifestation as a variant of Darier's disease.
Acantholysis ; Adolescent ; Biopsy ; Darier Disease ; Humans ; Keratins ; Male ; Nails ; Thumb

No abstract available.
Graft vs Host Disease* ; Liver Transplantation*

No abstract available.
Child* ; Heel* ; Humans

Cutaneous metastasis of visceral carcinomas is rare among them, endometrial carcinoma accounts for less than 1% of all cases. A 71-year-old woman with FIGO stage IIIA endometrial adenocarcinoma presented with scalp metastasis 1 month after initial radical radiotherapy. Histopathologic examination showed multiple glandular structures composed of columnar epithelial cells with foci of squamous differentiation, which were similar to primary endometrial adenocarcinoma. Metastatic evaluation revealed widespread extrapelvic metastasis in the lung, bones, and skin. Endometrial carcinoma is usually characterized by local and lymphatic spread. Rarely, extensive disease shows hematologic spread for example, to the scalp, as in this case.
Adenocarcinoma ; Aged ; Endometrial Neoplasms ; Epithelial Cells ; Female ; Humans ; Lung ; Neoplasm Metastasis ; Scalp ; Skin

We present a patient with various features of oculo-auriculo-vertebral syndrome (OAVS), also known as Goldenhar's syndrome. In general, multiple accessory tragi in a linear distribution from the preauricular skin to the mandible or to the lateral neck suggest a diagnosis of OAVS. However, in most cases, an accessory tragus is an isolated developmental defect without an associated congenital syndrome. A female infant presented with a solitary, skin colored, sessile papule on the right lower cheek, microtia, and ear deformity since birth. A biopsy specimen showed numerous irregularly spaced hair follicles with a prominent connective tissue framework in the subcutaneous fat, but without central cartilage. Multiple congenital anomalies, including ocular lipodermoid, sensorineural hearing loss, and vertebral deformity, were found on further evaluation.
Biopsy ; Cartilage ; Cheek ; Congenital Abnormalities ; Connective Tissue ; Ear ; Female ; Goldenhar Syndrome ; Hair Follicle ; Hearing Loss, Sensorineural ; Humans ; Infant ; Mandible ; Neck ; Parturition ; Skin ; Subcutaneous Fat

No abstract available.
Acinar Cells* ; Arthritis* ; Carcinoma, Acinar Cell* ; Humans ; Panniculitis*

No abstract available.
Eosinophilia ; Eosinophils ; Folliculitis ; Skin Diseases, Vesiculobullous ; Tacrolimus