1.Colonic Lymphangiomatosis Resolved after Excisional Biopsy.
Young Soo LEE ; Gyu Won KIM ; Hye Jae CHO ; Chan Sup SHIM
Clinical Endoscopy 2015;48(1):81-84
Lymphangioma is an uncommon malformation of the lymphatic system that involves a benign proliferation of the lymphatics, with no established treatment method. Multiple colonic lymphangioma, or colonic lymphangiomatosis, is an extremely rare condition. We report a case of colonic lymphangiomatosis that was detected during a colonoscopic examination conducted as part of a general health check-up. The lesion completely resolved after excisional biopsy.
Biopsy*
;
Colon*
;
Lymphangioma
;
Lymphatic System
2.Hennekam Syndrome: A Case Report
Yeong Guk LEE ; Seung Chan KIM ; Si Bog PARK ; Mi Jung KIM
Annals of Rehabilitation Medicine 2018;42(1):184-188
Hennekam syndrome is a rare autosomal recessive disorder resulting from malformation of the lymphatic system. The characteristic signs of Hennekam syndrome are lymphangiectasia, lymph edema, facial anomalies, and mental retardation. This is a case in which a patient presented with left-arm lymphedema, facial-feature anomalies, and multiple organ lymphangiectasia consistent with symptoms of Hennekam syndrome. There is no curative therapy at this time, but rehabilitative treatments including complete decongestive therapy for edema control appeared to be beneficial.
Edema
;
Humans
;
Intellectual Disability
;
Lymphatic System
;
Lymphedema
3.A Case of Fetal Nuchal Cystic Hygroma.
Yung Ha CHOI ; Chung Ok PARK ; Wan Seok PARK ; Tae Hyung LEE ; Sung Ho LEE
Yeungnam University Journal of Medicine 1989;6(1):165-169
Fetal cystic hygroma is a rare congenital malformation of the lymphatic system appearing as a single or multiloculated fluid-filled cavity, most often in the neck. A case of fetal nuchal cystic hygroma was diagnosed by Ultrasonography at 22 weeks of gestation and the diagnosis was confirmed at autopsy. We present the case with a brief review of literature.
Autopsy
;
Diagnosis
;
Lymphangioma, Cystic*
;
Lymphatic System
;
Neck
;
Pregnancy
;
Ultrasonography
4.Duodenal Lymphangioma.
Gyu Ha JUN ; Nak Hee KIM ; Bong Chun JUN ; Jung Min BAE ; Jong Dae BAE ; Ki Hoon JUNG
Journal of the Korean Surgical Society 2004;67(2):160-162
A lymphangioma is comparatively rare in the elimentary tract, and is a benign tumor of the lymphatic system. A duodenal lymphangioma is especially rare, and has an obscure etiology. Clinically, and in the laboratory the are non-specific, and are incidentally found by endoscopy, and their treatment is total excision. Recently, the authors experienced a 45 year-old woman, who had a duodenal lymphangioma, but with no symptom. An endoscopic examination revealed a single, about 2 cm, polypoid lesion below the ampulla. The lesion was successfully excised after a duodenotomy.
Duodenum
;
Endoscopy
;
Female
;
Humans
;
Lymphangioma*
;
Lymphatic System
;
Middle Aged
5.Retroperitoneal Lymphangioma Following Pyeloplasty in Child.
Dong Il KANG ; Se Jung JANG ; Jang Ho YOON ; Kyoung Soo HONG ; Soo Jin JUNG ; Yong Woo KIM ; Sung Hyup CHOI
Korean Journal of Urology 2005;46(1):86-88
A lymphangioma is a rare benign congenital tumor of the lymphatic system, resulting from the failure of lymphatic drainage into the venous system, which is due to atresia or the insufficiency of an efferent lymphatic channel. A lymphangioma usually occurs in the neck or axillary region. A retroperitoneal lymphangioma is very rare. Herein, a case of a retroperitoneal lymphangioma incidentally found four months after performing pyeloplasty on a child, is reported.
Child*
;
Drainage
;
Humans
;
Lymphangioma*
;
Lymphatic System
;
Neck
;
Retroperitoneal Space
6.One Case of Fetal Cystic Hygroma Diagnosed at the 11-1th Weeks of Gestational Age.
Byung Sun BAE ; You Me LEE ; Seung Joo SHIN ; Kyung Sub CAH
Korean Journal of Obstetrics and Gynecology 1997;40(2):434-438
Fetal cystic hygromas are congenital malformations of the lymphatic system manifested as single or multiloculated fluid-filled cavities in the neck region. Cystic hygroma is characterized by cystic appearance of posterior or lateral portion of the neck. A case of cystic hygroma, diagnosed antenatally by ultrasound at the 11(+1)th week of pregnancy and confirmed by autopsy, is presented with a brief review of literatures.
Autopsy
;
Gestational Age*
;
Lymphangioma, Cystic*
;
Lymphatic System
;
Neck
;
Pregnancy
;
Ultrasonography
7.Breast Lymphoma: A Report of 2 Cases.
Soo Jung LEE ; Jin Wook LEE ; Mi Soo HWANG ; Kil Ho CHO ; Bok Hwan PARK ; Dong Sug KIM
Journal of the Korean Radiological Society 1994;31(4):763-766
The diagnosis of breast lymphoma is a prime consideration when a breast mass develops in a patient with a history of lymphoma either in lymphatic system or at other anatomic sites, with bilateral axillary lymph nodes enlargment. However, the radiologic findings of lymphoma in breast are known as non-specific. Breast lymphoma is extremely rare and it has never been reported in this country. We report two cases of breast lymphoma with mammographic and sonographic findings.
Breast*
;
Diagnosis
;
Humans
;
Lymph Nodes
;
Lymphatic System
;
Lymphoma*
;
Ultrasonography
8.Radiofrequency Ablation of Microcystic Lymphatic Malformation in the Oral Cavity: 2 Case Studies.
Jae Woon WE ; Ki Beom BAE ; Jae Hwan KWON ; Joong Hwan CHO
Korean Journal of Otolaryngology - Head and Neck Surgery 2008;51(2):202-205
Lymphatic malformation is a congenital abnormality of the lymphatic system, which manifests frequently at birth or before 2 years of age. Lymphatic malformations are classified as macrocystic or microcystic. Microcystic lesions typically occur above the level of mylohyoid muscle and need conservative treatment rather than surgical resection because of the high rate of incomplete excision and recurrence. We report our experience with two cases of radiofrequency ablation of lymphatic malformation in the oral cavity recently seen in our practice.
Congenital Abnormalities
;
Lymphatic System
;
Mouth
;
Muscles
;
Parturition
;
Recurrence
9.Exosomes as a Communication Tool Between the Lymphatic System and Bladder Cancer.
Rebekah J PARK ; Yeo Jin HONG ; Yifan WU ; Paul Myungchul KIM ; Young Kwon HONG
International Neurourology Journal 2018;22(3):220-224
No abstract available.
Exosomes*
;
Lymphatic System*
;
Urinary Bladder Neoplasms*
;
Urinary Bladder*
10.Research progress in the cardiac lymphatic system and myocardial repair after myocardial infarction.
Tingyu DENG ; Zhaofeng SHI ; Yichao XIAO
Journal of Central South University(Medical Sciences) 2023;48(6):920-929
The lymphatic system of the heart plays an important role in the repair process after myocardial injury and may regulate normal tissue homeostasis and natural regeneration via maintaining fluid homeostasis and controlling the inflammatory response. The lymphatic system in the heart is activated after myocardial injury and is involved in the scarring process of the heart. Recent studies on the lymphatic system and myocardial repair of the heart have developed rapidly, and the mechanisms for lymphangiogenesis and lymphatic endothelial cell secretion have been elucidated by different animal models. A deep understanding of the structural, molecular, and functional characteristics of the lymphatic system of the heart can help develop therapies that target the lymphatic system in the heart. Summarizing the progress in studies on targets related to myocardial repair and the cardiac lymphatic system is helpful to provide potential new targets and strategies for myocardial repair therapy after myocardial infarction.
Animals
;
Heart
;
Myocardium
;
Myocardial Infarction
;
Heart Injuries
;
Lymphatic System