1.A pathologic study of abdominal lymphangiomas.
Jin Haeng CHUNG ; Yeon Lim SUH ; In Ae PARK ; Ja June JANG ; Je Geun CHI ; Yong Il KIM ; Woo Ho KIM
Journal of Korean Medical Science 1999;14(3):257-262
Abdominal lymphangiomas are uncommon angiomatous tumor occurring mainly in childhood. This is a retrospective clinicopathologic study of 17 cases of abdominal lymphangioma. The patients included are five children and 12 adults, with a mean age at initial presentation of 30.7 years (age ranges 3-63). The locations of the tumors were mesentery (5), retroperitoneum (4), colon (3), omentum (3), mesocolon (1) and gallbladder (1). Infiltrative growth was more common pattern than entirely circumscribed pattern. Masses were mostly multilocular cysts and contained chyle or serous fluid. On immunohistochemical staining, 16 cases were reactive for either CD31 or factor VIII-related antigen. These fact would suggest that intra-abdominal lymphangiomas simulate the immunohistochemical features of collecting lymphatics. Follow up was possible in 12 cases for 3-50 months (mean 19 months) and only one patient showed local recurrence. Although abdominal lymphangiomas are rare in adulthood and correct preoperative diagnosis is difficult, awareness of such a possibility in adulthood will contribute to make a correct preoperative diagnosis.
Abdominal Neoplasms/physiopathology
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Abdominal Neoplasms/pathology*
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Abdominal Neoplasms/metabolism
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Adult
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Antigens, CD31/biosynthesis
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Child
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Child, Preschool
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Factor VIII/biosynthesis
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Female
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Human
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Lymphangioma/physiopathology
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Lymphangioma/pathology*
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Lymphangioma/metabolism
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Male
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Middle Age
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Retrospective Studies
2.Giant adenomatoid neoplasm of the uters.
Wei-Bo MAO ; Yi-Ling ZHU ; Shao-Jie XU ; Yi-Xin LÜ
Chinese Journal of Pathology 2005;34(11):741-741
Adenomatoid Tumor
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metabolism
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pathology
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surgery
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Adult
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Biomarkers, Tumor
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metabolism
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Female
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Humans
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Hysterectomy
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methods
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Keratins
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metabolism
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Lymphangioma
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pathology
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Uterine Neoplasms
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metabolism
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pathology
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surgery
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Vimentin
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metabolism
3.Clinicopathologic features of fetal nuchal cystic hygroma: report of 40 cases.
Xiaobo ZHANG ; Yiqun GU ; Lijuan LU ; Yunfei SUN ; Yingnan WANG ; Aichun WANG ; Junling XIE
Chinese Journal of Pathology 2014;43(3):173-176
OBJECTIVETo study the pathogenesis, pathologic features and prognosis of fetal nuchal cystic hygroma.
METHODSForty autopsied cases of fetal nuchal cystic hygroma were collected during January 2003 to December 2012. The clinical history, pathologic changes and immunohistochemical (EnVision method) findings were reviewed, and the pathogenesis and pathologic characteristics were analyzed.
RESULTSOf the 40 cases, 16 (40.0%) showed single malformation and 24 (60.0%) were associated with multiple malformations in other organs and/or systems.Nineteen cases were septated and 21 were not. The associated malformations occurred in the respiratory system, skeletal system and urinary system.In the cases of combined malformations of umbilical cord, 3 were single umbilical artery malformations and 1 was torsion and stricture of umbilical cord.Four cases had chromosomal analysis, and all were trisomy-21.
CONCLUSIONSFetal nuchal cystic hygroma is a rare disease. The etiology is unknown, but it is not neoplastic.Lymphangioma is divided into 3 types:capillary lymphangioma, cavernous lymphangioma and cystic hygroma according to their expansile growth pattern. The overall prognosis is determined by any co-existing chromosomal anomalies, associated malformations and the time of diagnosis of the cystic hygroma.
Antibodies, Monoclonal, Murine-Derived ; metabolism ; Autopsy ; Calbindin 2 ; metabolism ; Female ; Fetus ; pathology ; Humans ; Hydrops Fetalis ; metabolism ; pathology ; Lymphangioma, Cystic ; metabolism ; pathology ; Male ; Pregnancy ; Pregnancy Outcome
4.MR imaging of hepatic lymphangioma.
Woo Jung CHOI ; Woo Kyoung JEONG ; Yongsoo KIM ; Jinoo KIM ; Ju Yeon PYO ; Young Ha OH
The Korean Journal of Hepatology 2012;18(1):101-104
No abstract available.
Aged
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Antigens, CD34/metabolism
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Female
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Humans
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Lymphangioma/pathology/*radionuclide imaging/ultrasonography
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Magnetic Resonance Imaging
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Tomography, X-Ray Computed
5.Splenic lymphangioma: clinicopathologic and immunohistochemical study of 18 cases and review of literature.
Xue-Feng TANG ; Wen-Yan ZHANG ; Gan-di LI ; Li-Li JIANG ; Wei-Ping LIU
Chinese Journal of Pathology 2007;36(2):98-101
OBJECTIVETo study the clinicopathologic features and differential diagnosis of splenic lymphangioma.
METHODSEighteen cases of splenic lymphangioma were retrieved from the pathology archives during the period between January 1990 to December 2005. The clinicopathologic features were analyzed. Immunohistochemical study was performed on the paraffin sections of 16 cases.
RESULTSThe age of the patients ranged from 9 to 72 years (median = 40 years). Thirteen patients were males and 5 were females. Clinically, the tumor could be asymptomatic or present with abdominal symptoms and hypersplenism. Follow-up information was available in 13 patients (72.2%) and the duration varied from 5 months to 15 years. All 13 patients had an uneventful clinical course, with no evidence of residual disease, local recurrence or metastasis. Gross examination showed splenic enlargement. The tumor appeared as cystic (8/18), solid (5/18) or honeycomb mass (5/18), either solitary (5/18) or multifocal (13/18). Histologically, splenic lymphangioma could be subclassified as cavernous (9/18), cystic (5/18) or mixed (4/18). Immunohistochemical study showed that the positivity rates for CD9 and D2-40 were 100% and 43.8% respectively.
CONCLUSIONSSplenic lymphangioma is a rarely encountered entity that can be misdiagnosed as a splenic hemangioma. A definite diagnosis depends on pathologic examination.
Adult ; Aged ; Antibodies, Monoclonal ; metabolism ; Antibodies, Monoclonal, Murine-Derived ; Antigens, CD ; metabolism ; Biomarkers, Tumor ; metabolism ; Child ; Diagnosis, Differential ; Female ; Follow-Up Studies ; Hemangioma ; metabolism ; pathology ; Humans ; Immunohistochemistry ; Lymphangioma ; metabolism ; pathology ; surgery ; Lymphangioma, Cystic ; metabolism ; pathology ; surgery ; Male ; Membrane Glycoproteins ; metabolism ; Middle Aged ; Splenectomy ; Splenic Neoplasms ; metabolism ; pathology ; surgery ; Tetraspanin-29