Pulmonary lymphangiectasis is relatively a rare disorder. This disorder can be divided into three groups. First, pulmonary abnormality is associated with lymphangiectasia in other viscera (especilly intestine) and extremities. In the second group, patients have a concomitant cardiac anomaly, which appears to be associated with obstructed pulmonary venous return. The third group comprises of patients whose lymphangicetasia is not associated with cardiac anomalies. This form is thought to result from abnormal development of the lung. In this case, a 6-year-old male who was previously diagnosed as lymphedema of extremities and intestinal lymphangiectasis, suffered from coughing and dyspnea repeatedly. High resolution computed tomography showed thickening of bronchovascular bundle and interlobular septa, pneumonic consolidation and pleural effusion. These findings were compatible with pulmonary lymphangiectasis. We report a case of pulmonary lymphangiectasis with brief review of literatures.
Child ; Cough ; Dyspnea ; Extremities ; Humans ; Lung ; Lymphangiectasis* ; Lymphangiectasis, Intestinal ; Lymphedema ; Male ; Pleural Effusion ; Viscera

Primary Intestinal lymphangiectasia (PIL) is a common cause of protein losing enteropathy (PLE). It will affect enter-hepatic circulation of lipid-soluble vitamin, and absorption of electrolytes, cause malnutrition related osteomalacia or osteoporosis. While seldom health care workers noted to assess and treat osteomalacia or osteoporosis in PIL. Here we report a related case. We found increased parathyroid hormone, decreased 25(OH)D3, low bone mineral density, which indicated that the PIL patient had osteomalacia and/or osteoporosis. Adequate calcium and vitamin D supply can relieve the condition efficaciously. We should pay attention to osteomalacia and osteoporosis in PIL patients.
Adolescent ; Female ; Humans ; Lymphangiectasis, Intestinal ; diagnosis ; Osteomalacia ; diagnosis ; Osteoporosis ; diagnosis

Female ; Humans ; Infant ; Lymphangiectasis, Intestinal ; diagnosis ; pathology ; therapy ; Male

Adolescent ; Child, Preschool ; Female ; Humans ; Lymphangiectasis, Intestinal ; Male

Adult ; Femoral Neck Fractures ; etiology ; Humans ; Lymphangiectasis, Intestinal ; complications ; therapy ; Male

Adult ; Aged ; Female ; Humans ; Intestine, Small ; surgery ; Lymphangiectasis, Intestinal ; pathology ; surgery ; Male ; Middle Aged

Adult ; Humans ; Intestine, Small ; pathology ; Liver Cirrhosis ; complications ; Lymphangiectasis, Intestinal ; etiology ; Male

CREB-Binding Protein/genetics* ; Humans ; Lymphangiectasis, Intestinal ; Rubinstein-Taybi Syndrome/genetics*

No abstract available.
Chylothorax* ; Lymphangiectasis*

Adult ; Drugs, Chinese Herbal ; therapeutic use ; Humans ; Ileal Diseases ; diagnosis ; therapy ; Lymphangiectasis, Intestinal ; diagnosis ; therapy ; Male ; Parenteral Nutrition