PURPOSE: Dandy-Walker syndrome is a rare congenital brain malformation that occurs one in every 25,000-35,000 live births, mostly in females. It is characterized by cystic enlargement of the fourth ventricle, agenesis or hypogenesis of the cerebellar vermis and enlargement of the posterior fossa. In this report, the authors aimed to address a rare case of a 14-months-old female Dandy-Walker syndrome patient that is presented with submucous cleft palate. METHODS: A 14-months-old female patient admitted to our outpatient clinic, via the department of pediatrics, with the complaints of nasal regurgitation, choking and breathing difficulties. She was diagnosed as Dandy-Walker syndrome by magnetic resonance imaging evaluation, at another hospital and underwent a shunt operation for the hydrocephalus continuing treatments. On physical examination, she had structural abnormality of bifid uvula, and palpable notch in the posterior surface of the hard palate. Her submucous cleft palate was corrected, which used a double opposing Z-plasty under general anesthesia. RESULTS: In a follow-up period of 2 months, no complications, such as wound dehiscence, necrosis and infection occurred, which shows satisfactory results. She consulted with pediatric neurologists and physical therapists for further evaluation and management of the abnormalities in the central nervous system. CONCLUSION: Dandy-Walker syndrome patient with a cleft palate is a very rare case to find, which only a few cases are reported around the world. Authors would like to share this case of Dandy-Walker syndrome patient, with submucous cleft palate, who underwent a double opposing Z-plasty that shows satisfactory results.
Airway Obstruction ; Ambulatory Care Facilities ; Brain ; Cleft Palate ; Dandy-Walker Syndrome ; Female ; Follow-Up Studies ; Fourth Ventricle ; Humans ; Hydrocephalus ; Live Birth ; Magnetic Resonance Imaging ; Necrosis ; Palate, Hard ; Pediatrics ; Physical Examination ; Physical Therapists ; Respiration ; Uvula

PURPOSE: Dandy-Walker syndrome is a rare congenital brain malformation that occurs one in every 25,000-35,000 live births, mostly in females. It is characterized by cystic enlargement of the fourth ventricle, agenesis or hypogenesis of the cerebellar vermis and enlargement of the posterior fossa. In this report, the authors aimed to address a rare case of a 14-months-old female Dandy-Walker syndrome patient that is presented with submucous cleft palate. METHODS: A 14-months-old female patient admitted to our outpatient clinic, via the department of pediatrics, with the complaints of nasal regurgitation, choking and breathing difficulties. She was diagnosed as Dandy-Walker syndrome by magnetic resonance imaging evaluation, at another hospital and underwent a shunt operation for the hydrocephalus continuing treatments. On physical examination, she had structural abnormality of bifid uvula, and palpable notch in the posterior surface of the hard palate. Her submucous cleft palate was corrected, which used a double opposing Z-plasty under general anesthesia. RESULTS: In a follow-up period of 2 months, no complications, such as wound dehiscence, necrosis and infection occurred, which shows satisfactory results. She consulted with pediatric neurologists and physical therapists for further evaluation and management of the abnormalities in the central nervous system. CONCLUSION: Dandy-Walker syndrome patient with a cleft palate is a very rare case to find, which only a few cases are reported around the world. Authors would like to share this case of Dandy-Walker syndrome patient, with submucous cleft palate, who underwent a double opposing Z-plasty that shows satisfactory results.
Airway Obstruction ; Ambulatory Care Facilities ; Brain ; Cleft Palate ; Dandy-Walker Syndrome ; Female ; Follow-Up Studies ; Fourth Ventricle ; Humans ; Hydrocephalus ; Live Birth ; Magnetic Resonance Imaging ; Necrosis ; Palate, Hard ; Pediatrics ; Physical Examination ; Physical Therapists ; Respiration ; Uvula

Takayasu's disease is characterized by absent upper extremity pulses and ophthalmological finding of secreased visions and catract formation. Clinical features of Takayasu's disease are attributed to an obstructive arteritis of the large vessels criginating from aortic arch and other aortic segments. This dissease most frequently has been reported from Orient, and has affected primarily young females. This is a report of a 10 years old girl who developed the typical clinical and pathophysiological manifestation of Takayasu's disease and we also made brief review of literature.
Aorta, Thoracic ; Arteritis ; Child ; Female ; Humans ; Upper Extremity

Bladder rupture following blunt trauma is rare, and no neobladder rupture following blunt trauma has yet been reported. We present a case of neobladder rupture following blunt trauma. The patient was a 65-year-old male patient who had been treated for bladder cancer via a radical cystectomy with an orthotopic ileal neobladder four years prior to this admission, and who was admitted to our emergency department due to multiple trauma after a 1.5 m fall. Primary repair was performed for the neobladder rupture.
Aged ; Cystectomy ; Emergencies ; Humans ; Male ; Multiple Trauma ; Rupture ; Urinary Bladder ; Urinary Bladder Neoplasms

Distant metastasis of a colon carcinoma in situ has not yet been reported. We experienced a case of a sigmoid colon carcinoma in situ with common hepatic lymph node metastasis. After the first operation, we diagnosed dual intramucosal adenocarcinomas of the sigmoid colon without any regional lymph node metastasis. After the second operation, a metastatic adenocarcinoma was found in the common hepatic lymph nodes. We suggest that metastasis in cases of a colonic carcinoma in situ is rare, but possible. The parallel progression model of tumors can explain this early metastasis.
Adenocarcinoma ; Carcinoma in Situ ; Colon ; Colon, Sigmoid ; Colonic Neoplasms ; Lymph Nodes ; Lymphatic Metastasis ; Neoplasm Metastasis ; Sigmoid Neoplasms*

In this study, immunohistochemistry was used to examine the changes in the density of colonic endocrine cells - argyrophil and argentaffin cells, chromogranin A (CGA), serotonin, somatostatin and glucagon-containing cells in trinitrobenzene sulfonic acid (TNBS)-induced rat colitis. Ulcerative colitis was induced by the instillation of 10 mg of TNBS into the colonic lumen through the anus. To confirm the inducement of ulcerative colitis, the macroscopic and microscopic scores as well as the colonic myeloperoxidase (MPO) activities were monitored for 8 days after TNBS instillation in the colonic lumens. In addition, the number of argyrophil and argentaffin cells, CGA, serotonin, somatostatin and glucagon-immunoreactive cells were counted in the colonic mucosa, respectively. After TNBS instillation into the lumen of the colon from the anus in rats, increases in macroscopic and microscopic scores in the colon tissues were observed along with increases in the colonic MPO activities. Therefore, ulcerative colitis was relatively well induced by the TNBS instillations. Marked decreases in the number of colonic endocrine cells were detected in the TNBS-treated animal compared to the sham control. These results suggest that colonic endocrine cells were also disrupted by TNBS-induced ulcerative colitis.
Anal Canal ; Animals ; Chromogranin A ; Colitis ; Colitis, Ulcerative ; Colon ; Endocrine Cells ; Enterochromaffin Cells ; Immunohistochemistry ; Mucous Membrane ; Peroxidase ; Rats ; Salicylamides ; Serotonin ; Somatostatin

Trauma is frequently not purely penetrating or purely blunt. Such mixed trauma can result from the mechanism of injury. Recently, we encountered a patient who accidentally shot himself with a shotgun. He had a 15 x 8-cm-sized penetrating injury on left flank that did not penetrate into the peritoneal cavity and a blunt splenic injury with hemoperitoneum. Surgical and interventional treatments were performed for each injury. We present this case with a review of the related literature.
Hemoperitoneum ; Humans ; Peritoneal Cavity

PURPOSE:The purpose of this study was to determine the prevalence of asthma, allergic rhinitis, atopic dermatitis and allergic conjunctivitis among primary school pupils in Ilsan, Gyeonggi province. We also investigated change of symptoms after environmental control. METHODS:In April 2005, a cross-sectional study was performed among 2,745 1st to 6th graders of 3 primary schools in Ilsan, Gyeonggi province. International Study of Asthma and Allergies in Childhood (ISAAC) standardized questionnaires and additional questionnaires about environmental changes were distributed to their parents. RESULTS:Data were collected from 2,535 children (1,279 boys and 1,256 girls). The most common allergic symptom was rhinorrhea (43.0%), and atopic skin lesions, ocular lesions and wheezing were 24.5%, 19.7% and 18.2%, respectively. There was no significant relationship between allergic diseases and environmental status. One thousand four hundred nineteen children moved to a new place or had new interior decorations within the last 2 years. Of these children, 352 (24.8%) had allergic symptoms (OR=2.76, CI= 1.96-3.41, P=0.001). Interestingly, we found that children who had moved into apartments experienced more symptom changes than those who had not (P=0.022). CONCLUSION:The results of this study demonstrated that the prevalence of allergic conditions in primary school children in Ilsan, Gyeonggi province in 2005 was higher than those of nation-wide studies in 2000. We found the results of our study is similar to those of Seoul in 2005. We found a significant relationship between environmental status and changes of symptoms in primary school children in Ilsan, Gyeonggi province.
Asthma ; Bronchial Hyperreactivity ; Child* ; Conjunctivitis, Allergic ; Cross-Sectional Studies ; Dermatitis, Atopic ; Gyeonggi-do* ; Humans ; Hypersensitivity ; Parents ; Prevalence* ; Pupil ; Surveys and Questionnaires ; Respiratory Function Tests ; Respiratory Sounds ; Rhinitis ; Seoul ; Skin

PURPOSE:The purpose of this study was to determine the prevalence of asthma, allergic rhinitis, atopic dermatitis and allergic conjunctivitis among primary school pupils in Ilsan, Gyeonggi province. We also investigated change of symptoms after environmental control. METHODS:In April 2005, a cross-sectional study was performed among 2,745 1st to 6th graders of 3 primary schools in Ilsan, Gyeonggi province. International Study of Asthma and Allergies in Childhood (ISAAC) standardized questionnaires and additional questionnaires about environmental changes were distributed to their parents. RESULTS:Data were collected from 2,535 children (1,279 boys and 1,256 girls). The most common allergic symptom was rhinorrhea (43.0%), and atopic skin lesions, ocular lesions and wheezing were 24.5%, 19.7% and 18.2%, respectively. There was no significant relationship between allergic diseases and environmental status. One thousand four hundred nineteen children moved to a new place or had new interior decorations within the last 2 years. Of these children, 352 (24.8%) had allergic symptoms (OR=2.76, CI= 1.96-3.41, P=0.001). Interestingly, we found that children who had moved into apartments experienced more symptom changes than those who had not (P=0.022). CONCLUSION:The results of this study demonstrated that the prevalence of allergic conditions in primary school children in Ilsan, Gyeonggi province in 2005 was higher than those of nation-wide studies in 2000. We found the results of our study is similar to those of Seoul in 2005. We found a significant relationship between environmental status and changes of symptoms in primary school children in Ilsan, Gyeonggi province.
Asthma ; Bronchial Hyperreactivity ; Child* ; Conjunctivitis, Allergic ; Cross-Sectional Studies ; Dermatitis, Atopic ; Gyeonggi-do* ; Humans ; Hypersensitivity ; Parents ; Prevalence* ; Pupil ; Surveys and Questionnaires ; Respiratory Function Tests ; Respiratory Sounds ; Rhinitis ; Seoul ; Skin

Arteriovenous malformation (AVM) of the pancreas is extremely rare, although it may be increasingly diagnosed due to the widespread use of cross-sectional imaging of the abdomen. Early diagnosis of this disease is important to prevent delay of treatment and resulting fatal complications. We report a rare case of pancreatic AVM in a 48-year-old man who presented with severe chronic anemia and early gastric cancer, which made diagnosis challenging. Imaging findings, including ultrasound, computed tomography, and magnetic resonance imaging, are shown, as well as the pathologic features.
Abdomen ; Anemia ; Arteriovenous Malformations* ; Diagnosis ; Early Diagnosis ; Hemorrhage* ; Humans ; Magnetic Resonance Imaging ; Middle Aged ; Pancreas ; Pancreaticoduodenectomy ; Stomach Neoplasms* ; Ultrasonography