Cystinuria is an autosomal recessive inherited defect in renal tubular reabsorption of four amino acids, cystine, ornithine, lysine and arginine. Homozygotes were identified by the formation of urinary tract calculi composed of cystine and by gross hyperexcretion of above mentioned four amino acids. Urinary tract calculi composed primarily of cystine are rare in adults and children. These are usually pure and found exclusively in patients with cystinuria. Herein we report on a 4 and 3/12 years old male child with a right renal stone composed primarily of cystine which was confirmed by chemical analysis method postoperatively. After discharge he has been treated with D-penicillamine, large fluid intake and conversion of urine pH.
Adult ; Amino Acids ; Arginine ; Calculi ; Child* ; Cystine* ; Cystinuria ; Homozygote ; Humans ; Hydrogen-Ion Concentration ; Lysine ; Male ; Ornithine ; Penicillamine ; Urinary Tract

Rhadomyosarcoma of the prostate is relatively rare and highly malignant condition. Three major categories of rhabdomyosarcoma exist, which should be kept clearly separated: pleomorphic, embryonal, and alveolar Pleomorphic rhabdomyosarcoma is actually the least common of the three categories. It arises from myotome-derived skeletal muscle and occurs almost exclusively in adults. We make the unequivocal diagnosis of pleomorphic rhabdomyosarcoma only if we can detect cross striations in some of the tumor cells. Herein we experienced a pleomorphic rhabdomyosarcoma of the prostate which is generally not found in the urogenital area and reviewed literature briefly.
Adult* ; Diagnosis ; Humans ; Muscle, Skeletal ; Prostate* ; Rhabdomyosarcoma*

OBJECTIVES: To investigate the differences in accessing regional hospitals and the utilization rate of hospitals located in other regions for cancer patients by regions. METHODS: Data for the utilization of regional hospitals for cancer patients were obtained from the Korean National Cancer Incidence Databases in 1999 and 2002. We divided the regions into 16 provinces by administrative districts. We using the SAS 9.1.3 to analyze difference of regional self-sufficiency and the Arcview 3.2 to show in a schematize for regional variation of the regional self-sufficiency. RESULTS: There were regional variations in the regional self-sufficiency of cancer patients. Especially, Jeollanam-do(1999 13.6%, 2002 12.8%), Gyeongsangbuk-do(1999 22.0%, 2002 20.7%), and Chungcheongnam-do(1999 27.8%, 2002 27.1%) had low regional self-sufficiency. The regional self-sufficiency in Gyeonggi-do and utilization rate of cancer patients who lived in other regions were increased between 1999 and 2002(regional self-sufficiency: 1999 37.2%, 2002 48.2%). CONCLUSION: The results of this study showed that there were regional variation in utilization of regional hospitals for cancer patients. Accessibility of cancer patients in metropolitan areas was higher than in small size cities, medium size cities, and rural county areas. These results suggested that it should be considered support medical facilities for cancer patients in rural areas where have lower relevance rate.
Gyeonggi-do ; Humans ; Incidence