No abstract available.
Klippel-Trenaunay-Weber Syndrome*

No abstract available.
Humans ; Klippel-Trenaunay-Weber Syndrome

No abstract available.
Anal Canal* ; Klippel-Trenaunay-Weber Syndrome*

Klippel-Trenaunay syndrome is a rare congenital vascular disorder characterized by cutaneous hemangioma, multiple varicosities, and hypertrophy of involved extremities. It is rarely associated with bladder hemangioma. The authors report the imaging findings of a case of the Klippel-Trenaunay syndrome involving hemangioma of the bladder.
Extremities ; Hemangioma* ; Hypertrophy ; Klippel-Trenaunay-Weber Syndrome* ; Urinary Bladder*

Klippel-Trenaunay syndrome (KTS) is a rare congenital disorder and is essentially a disorder of capillary, venous, and lymphatic malformations. Hematochezia is the most common symptom associated with intestinal hemangiomatosis and remains one of the life-threatening emergencies in KTS. We reported one patient of KTS presented with rectal bleeding and severe anemia who was successfully managed by sphincter-saving operation.
Anemia ; Capillaries ; Congenital, Hereditary, and Neonatal Diseases and Abnormalities ; Emergencies ; Gastrointestinal Hemorrhage ; Hemorrhage ; Humans ; Klippel-Trenaunay-Weber Syndrome

Two cases of Klippel-Trenaunay-Weber Syndrome were presented and its literatures were reviewed. The patients were 25 year old male farmer and 38 year old housewife. Both had hypertrophy, port-wine nevus, and varicosities in case 1, on left lower extremity since birth. The length and cirumference of the affected leg were longer than the other side, and X-ray showed osteohypertrophy of tibia of the involved leg,
Adult ; Humans ; Hypertrophy ; Klippel-Trenaunay-Weber Syndrome* ; Leg ; Lower Extremity ; Male ; Nevus ; Parturition ; Tibia

Two cases of Klippel-Trenaunay-Weber Syndrome were presented and its literatures were reviewed. The patients were 25 year old male farmer and 38 year old housewife. Both had hypertrophy, port-wine nevus, and varicosities in case 1, on left lower extremity since birth. The length and cirumference of the affected leg were longer than the other side, and X-ray showed osteohypertrophy of tibia of the involved leg,
Adult ; Humans ; Hypertrophy ; Klippel-Trenaunay-Weber Syndrome* ; Leg ; Lower Extremity ; Male ; Nevus ; Parturition ; Tibia

Klippel-Trenaunay syndrome (KTS) is a rare congenital malformation syndrome involving blood and lymph vessels, which is characterized by triad of cutaneous hemangioma, venous varicosities, and overgrowth of the affected limbs. Because vascular malformation in KTS can be located anywhere except the face and brain, the clinical presentation could be extremely variable. But there are only rare case reports that KTS is associated with spinal cord lesion. We report a case of recurrent myelopathy in a patient with KTS.
Brain ; Extremities ; Hemangioma ; Humans ; Klippel-Trenaunay-Weber Syndrome* ; Spinal Cord ; Spinal Cord Diseases* ; Vascular Malformations

Pseudo-Kaposi's sarcoma is an unusual cutaneous sequelae of chronic venous insufficiency and congenital vascular malformation of the lower extremities. It is a benign vascular process encountered on the lower extremities, which resembles a superficial form of stasis dermatitis, however, is clinically characterized by circumscribed violaceous, brown or dusky papules and plaques. We, herein, report a case of unilateral pseudo-Kaposi's sarcoma associated with Klippel-Trenaunay syndrome.
Dermatitis ; Klippel-Trenaunay-Weber Syndrome* ; Lower Extremity ; Sarcoma* ; Vascular Malformations ; Venous Insufficiency

Klippel-Trenaunay-Weber syndrome is a rare, sporadically occuring disorder characterized by hemihypertrophy (unilateral limb hypertrophy), varicose veins, hemangiomata and occasionally arteriovenous malformation. With the development of ultrasonography, this syndrome can be detected by antenatal sonography. We report a case of Klippel-Trenaunay-Weber syndrome that demonstrates huge mass with increased blood flow on left thigh detected by ultrasonography.
Arteriovenous Malformations ; Extremities ; Klippel-Trenaunay-Weber Syndrome* ; Thigh ; Ultrasonography* ; Varicose Veins