No abstract available.
Myasthenia Gravis*

No abstract available.
Transplants*

No abstract available.
Acrocephalosyndactylia* ; Hypertelorism* ; Orbit*

No abstract available.
Graft Survival* ; Transplants*

We experienced a case of brainstem encephalitis that is possibly caused by herpes simplex virus infection in a 3 year-old girl. The diagnosis was made by clinical symptoms, neurologic exam, serologic test, brain CT, brain MRI and brainstem biopsy. Herpes simplex virus specific antibody was detected from cerebrospinal fluid and the titer was 11.78 by enzyme immunoassay. Stereotaxic brainstem biopsy was done for differenciate from brainstem glioma at 24th hospital day. Patient was treated with acyclovir and improved in association with neurologic sequallae at 3 months later. Brief review of literatures was made.
Acyclovir ; Biopsy ; Brain ; Brain Stem* ; Cerebrospinal Fluid ; Child, Preschool ; Diagnosis ; Encephalitis* ; Female ; Glioma ; Humans ; Immunoenzyme Techniques ; Magnetic Resonance Imaging ; Neurologic Manifestations ; Serologic Tests ; Simplexvirus

Epidermoid cyst originating within the diploic space of the bony orbit is rare. The authors describe two cases of epidermoid cyst of the orbit. The clinical presentation was dependent on the location of the slowly expanding epidermoid cyst. Proptosis caused by intraorbital extension of the mass was the presenting sign in both case. The finding in orbit CT scan appeared to be specific for intradipolic epidermoid cyst. Their clinical presentations and surgical management were briefly discussed.
Epidermal Cyst ; Exophthalmos ; Orbit* ; Tomography, X-Ray Computed

Hemifacial spasm is a relatively uncommon but distressing condition characterized by insiduous development of paroxysmal, involuntary, unilateral hyperkinetic facial movement. In patients with hemifacial spasm, there is an abnormality in the facial nerve or its nucleus which allows the stimulus applied to one branch of the facial nerve to spread to other branches of that same nerve. This lateral spread response is presumed to be due to cross transmission of the antidromic activity in the branch of the facial nerve, and intraoperative monitoring of lateral spread responses provides a useful way of confirming complete facial nerve decompression. In 17 consecutive patients, intraoperative electromyographic(EMG) recordings were made from facial muscles during microvascular decompression for hemifacial spasm. At the beginning of the operation, electrical stimulation of the temporal or zygomatic branch of the facial nerve gave rise to electrically recordable activity in the mentalis muscle(lateral spread), with a latency of about 10msec, that in ten patients, lasted until the facial nerve was decompressed; In seven patients, however, it disappeared when the arachnoid membrane was opened. Early disappearance of lateral spread was frequently occurred in single offending vessel or cases where there was loose compression. Postsurgically the 16 patients in whom the lateral spread response disappeared totally were free from spasm after the operation and in the remaining patient, there was much improvement. These results support the use of lateral spread response monitoring during decompression surgery for hemifacial spasm, and provide strong circumstantial evidence that vascular cross-compression is an important etiologic factor in hemifacial spasm. During a decompression operation for hemifacial spasm, the authors now routinely monitor facial EMG response.
Arachnoid ; Decompression* ; Electric Stimulation ; Facial Muscles ; Facial Nerve ; Hemifacial Spasm* ; Humans ; Membranes ; Microvascular Decompression Surgery ; Monitoring, Intraoperative ; Spasm

No abstract available.
Syringomyelia*

OBJECTIVES: This study investigated whether the impacts of orthodontic treatment of malocclusion on oral health-related quality of life and happiness are positive with middle and high school students. METHODS: Subjects were 157 orthodontic patients and 83 non-orthodontic in malocclusion patients. Questionnaires were collected with the self-administered method, and consisted of the general characteristics, self-esteem, social support appraisal scale(friends, family, teacher), Oral Impact on Daily Performance (OIDP) and oxford happiness questionnaire (OHQ). RESULTS: A physical factor was lower in the orthodontic treatment group (5.8±2.48) than in the non-orthodontic treatment group (7.7±2.10)(p<0.001), and OIDP was lower in the orthodontic treatment group (7.0±1.79) than in the non-orthodontic treatment group (7.8±1.80)(p=0.002). A feeling of happiness was higher in the orthodontic treatment group(4.6±0.81) than in the orthodontic treatment group (4.3±0.89) (p=0.009). As results of multiple regression analysis, OIDP was affected of orthodontic treatment(β=−0.0222, p=0.001) and OHP was affected of orthodontic treatment(β=0.087, p=0.030) and OIDP(β=0.116, p=0.003). CONCLUSIONS: Orthodontic treatment of malocclusion may positively affects happiness in teenager. Support policy for orthodontic treatment of malocclusion is necessary for adolescents.
Adolescent ; Happiness* ; Humans ; Malocclusion* ; Methods ; Quality of Life

We experienced a case of primary sclerosing cholangitis(PSC) in a 40-year-old female who complained of jaundice and pruritus. Marked elevation of serum alkaline phophatase level, typical beaded appearance and pruned-tree appearance on endoscopic retrograde cholangiography, together with a finding of chronic obliterative fibrosing cholangitis on sono-guided gun biopsy specimen of the liver led to a confirmative diagnosis of PSC. The patient responded to ursodeoxycholic acid (UDCA), but was reluctant to treatment and died of hepatic failure 7 months later. PSC is a very rare disease in Korea. So far, only 5 cases including our present case have been reported in the Korean literature. Male-to-female ratio was 2:3 and the median age was 40(27-80 years old). Ulcerative colitis was associated in one case. Four cases involved both intra, and extrahepatic bile ducts and one case was reported to be confined in the intrahepatic bile ducts. Fatality was in 3 cases, 20 days, 36 days, and 7 months after the initial presentaion, respectively. The causes of death were acute cholangitis and sepsis in two, and hepatic failure in one. We herein report a case of PSC and clinical charateristics of the reported cases in Korea, and review the literature with an emphasis on UDCA treatment in PSC.
Adult ; Bile Ducts, Extrahepatic ; Bile Ducts, Intrahepatic ; Biopsy ; Cause of Death ; Cholangiography ; Cholangitis ; Cholangitis, Sclerosing* ; Colitis, Ulcerative ; Diagnosis ; Female ; Humans ; Jaundice ; Korea ; Liver ; Liver Failure ; Pruritus ; Rare Diseases ; Sepsis ; Ursodeoxycholic Acid