1.Spontaneous Aortic Dissection in a Patient with Neurofibromatosis.
Jin Bae LEE ; Min Sik PARK ; Sung Chang JUNG ; Sung Hun PARK ; Myoung In JIN ; Sang Hyuk LIM ; Seung Hie CHUNG ; Jun Yerb LEE ; Jae Kean RYU ; Ji Yong CHOI ; Sung Cug CHANG
Korean Circulation Journal 2003;33(1):68-71
Neurofibromatosis type 1 (NF-1), or von Recklinhausen's disease, is an autosomal dominant disorder that primarily affects the skin, the central and peripheral nervous systems, and the skeleton. Vasculopathy, such as, aneurysm or stenosis of large vessels is a less common manifestation of NF-1, but spontaneous aortic dissection in NF-1 is very rare. We report a case of acute aortic dissection with incidental aneurysm of the right femoral artery in NF-1.
Aneurysm
;
Constriction, Pathologic
;
Femoral Artery
;
Humans
;
Neurofibromatoses*
;
Neurofibromatosis 1
;
Peripheral Nervous System
;
Skeleton
;
Skin
Result Analysis
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