No abstract available.
Sturge-Weber Syndrome*

Chronic mucocutaneous randidiasis is a clinical syndrome characte ized by chronic and reccurent superficial candidal infection of the skin, mucous membranes, and nails. This syndrome is frequently associated with immune deficiency or endocrinopathy, especially hypopar; thyroidism. We report a case of chrcinic mucocutaneous candidiasis associated with hypoparathyroidism in a 8- year-old girl.
Candidiasis ; Candidiasis, Chronic Mucocutaneous* ; Female ; Humans ; Hypoparathyroidism* ; Mucous Membrane ; Skin ; Thyroid Gland

BACKGROUND: Urticaria pigmentosa(UP) is primarily a disease of children. There have been no clinical studies of UP in Korea. OBJECTIVE: This study was performed to find the clinical characteristics of UP in Korean child-hood patients. METHOD: Twenty-nine cases of urticaria pigmentosa confirmed clinically and histopathologically were analyzed. RESULTS: The maculopapular type was the most common with the usual age of onset before the age of 6 months, and the lesions tended to be distributed in the central portion of the body. Darier sign was positive in 92% of the patients(24/26). No systemic involvements were detected in any of the patients with minimal associated symptoms. Seven patients of the maculopapular type and one patient of the multiple nodular type followed up for more than 2 years showed a tendency to improve or clear by the age of 6 years. CONCLUSION: Neonatal or infantile-onset patients of UP in Korean pediatric population were considered to have a benign clinical course and to require no aggressive therapy.
Age of Onset ; Child* ; Clinical Study* ; Humans ; Korea ; Methods ; Urticaria Pigmentosa* ; Urticaria*

No abstract available.

No abstract available.
Microvascular Decompression Surgery*

Leiomyoma is rare. Most of patients present with urinary tract infection, hematuria, dyspareunia, or complaint of mass. A case of leiomyoma on urethrovaginal septum in a 36 years old female was presented. The presenting symptom was a protruding mass at the anterior vaginal wall The mass was removed surgically and confirmed as a leiomyoma pathologically.
Adult ; Dyspareunia ; Female ; Hematuria ; Humans ; Leiomyoma* ; Urinary Tract Infections

The pulsed laser lithotripsy has been used in the treatment of urinary calculi. We treated 153 patients of stones, via the pulsed dye laser(Technomed Pulsolith) with 7.5 and 6.5 F. rigid ureteroscope between January 1992 and January 1995. Stones were in bladder(4 cases), upper ureter(17), mid ureter(31) and lower ureter(101). The laser lithotripsies were applied for impacted stones and relatively large stones(more than 6 mm) The success rates according to location were 47%(8/17) in upper ureter, 77%(24/31)in middle ureter, 95%(96/101)in lower ureter and 100%(4/4) in bladder and mean success rate was 86% (132/153). There were 21 failures due to upward migration(9 cases), poor visual field(7), laser resistant stone(3) and malfunction of laser(2). Complications were showed in 28 cases that were gross hematuria(16 cases), ureteral perforation(6), fever(4) and ileus(2), but most of them might be related to ureteroscopy rather than laser, and all of them were resolved with conservative management. So laser lithotripsy is safe and effective method of middle and lower ureteral calculi, and upward migration of stones, the major cause of failure may be resolved by use of extracorporeal shock wave lithotripsy and flexible ureteroscope.
Humans ; Lithotripsy ; Lithotripsy, Laser* ; Shock ; Ureter ; Ureteral Calculi ; Ureteroscopes ; Ureteroscopy ; Urinary Bladder ; Urinary Calculi

Nocturnal penile tumescence has been proposed as a source of objective data in the evaluation of erectile capacity and clinically important in differentiating between psychogenic and organic impotence. However, the absence of sleep information and difficult differentiation of movement artifact leads to false positive or false negative reaction when portable home monitor is used. This can be overcome by polysomnographic monitoring. In addition, sleep disorders affecting nocturnal penile tumescence also could be screened. Herein, we conducted a study to investigate the significance of polysomnographic nocturnal penile tumescence monitoring in 45 men with erectile dysfunction. The nocturnal penile tumescence data from polysomnographic method were compared with those from portable method, based on the results from standard method. The results obtained were summarized 1. Polysomnographic method showed higher sensitivity(82%), lower false positive(20%) and false negative rate(16%) than portable method (71%, 30%, 28%, respectively) in the differential diagnosis of impotence. 2. Among 10 patients, with measuring of air flow monitoring and anterior tibialis EMG one patient had periodic leg movement. 3. Statistically, parameters of total REM time, total tumescence time/total sleep time, number of maximum tumescence episodes, amount of maximum tumescence episodes, T-up and T-max phase in maximum tumescence episodes, circumferential changes in maximum tumescence episodes, and rigidity in maximum tumescence episodes were found to be significantly decreased in organic impotence group. These results reflect that polysomnographic NPTM provides more validity than portable NPTM on the outcome of the differential diagnosis of impotence, and it would contribute to screening of occult sleep disorders and to study for their characteristics in association with impotence.
Artifacts ; Diagnosis* ; Diagnosis, Differential ; Erectile Dysfunction* ; False Negative Reactions ; Humans ; Leg ; Male ; Mass Screening ; Penile Erection* ; Sleep Wake Disorders

To investigate hemodynamic mechanism of penile erection and to establish animal model which permits hemodynamic study, simultaneous measurement of flow rate, pressure of the internal pudendal artery, and intracorporeal pressure during penile erection was performed using canine electroerection models. The results obtained were summarized as followings: 1. Following pelvic nerve stimulation, the erection phenomenon was grossly observed. The intracorporeal pressure began to increase after a latent period of mean 11.3 sec., and increased to the maximum and then maintained plateau state. When the stimulation was terminated, detumescence with gradual decrease of intracorporeal pressure was observed. 2. With stimulation above threshold level, transient drop of intracorporeal pressure was observed immediately after stimulation. The latent period and time to the maximal intracorporeal pressure were shortened. However, the degree of maximal intracorporeal pressure was not changed. 3. Following electric stimulation of the pelvic nerve, immediate decrease in internal pudendal arterial pressure and increase in flow rate of the internal pudendal artery without change in systemic blood pressure were followed by gradual increase in intracorporeal pressure. These indicate that relaxation of the sinusoidal smooth muscles and the arteries supplying the corpus cavernosum by pelvic nerve stimulation results in an increase in arterial inflow to the corpus cavernosum, which would play an important role in induction of penile erection. And it is suggested that this animal model would contribute to further hemodynamic study and development of therapeutics in erectile impotence.
Animals ; Arterial Pressure ; Arteries ; Blood Pressure ; Dogs* ; Electric Stimulation ; Erectile Dysfunction ; Hemodynamics* ; Male ; Models, Animal ; Muscle, Smooth ; Penile Erection* ; Relaxation

To investigate hemodynamic mechanism of penile erection and to establish animal model which permits hemodynamic study, simultaneous measurement of flow rate, pressure of the internal pudendal artery, and intracorporeal pressure during penile erection was performed using canine electroerection models. The results obtained were summarized as followings: 1. Following pelvic nerve stimulation, the erection phenomenon was grossly observed. The intracorporeal pressure began to increase after a latent period of mean 11.3 sec., and increased to the maximum and then maintained plateau state. When the stimulation was terminated, detumescence with gradual decrease of intracorporeal pressure was observed. 2. With stimulation above threshold level, transient drop of intracorporeal pressure was observed immediately after stimulation. The latent period and time to the maximal intracorporeal pressure were shortened. However, the degree of maximal intracorporeal pressure was not changed. 3. Following electric stimulation of the pelvic nerve, immediate decrease in internal pudendal arterial pressure and increase in flow rate of the internal pudendal artery without change in systemic blood pressure were followed by gradual increase in intracorporeal pressure. These indicate that relaxation of the sinusoidal smooth muscles and the arteries supplying the corpus cavernosum by pelvic nerve stimulation results in an increase in arterial inflow to the corpus cavernosum, which would play an important role in induction of penile erection. And it is suggested that this animal model would contribute to further hemodynamic study and development of therapeutics in erectile impotence.
Animals ; Arterial Pressure ; Arteries ; Blood Pressure ; Dogs* ; Electric Stimulation ; Erectile Dysfunction ; Hemodynamics* ; Male ; Models, Animal ; Muscle, Smooth ; Penile Erection* ; Relaxation