Congenital M llerian anomalies of uterus are so infrequently encountered and endometriosis, primary infertility, hematometra, and urinary tract anomalies are claimed to be common complaints in women with unicornuate uterus. We report one case of rudimentary horn associated with agenesis of right kidney and pelvic endometriosis which is presented with brief review of literature about anomaly of the female genital tract.
Animals ; Endometriosis* ; Female ; Hematometra ; Horns* ; Humans ; Infertility ; Kidney* ; Urinary Tract ; Uterus

Uterine torsion is defined as the mtation of more than 45 degrees around the long axis of the uterus or a rotation which is severe enough to produce symptoms. Torsion of the human pregnant uterus is a very rare complication. The diagnosis is problematic and is often made during a cesrean section due to inhibited labor. Torsion of the human pregnant uterus can be caused by myoma or other uterine abnormalities, ovarian cysts, adhesions, abnormal fetal presentations, or fetal abnormalities ( though no cause can be found in about 20% of cases ). Uterine torsion produces symptoms of varying severity depending on the degree of rotation, and duration of the pregnancy. High mortality rates for both mother and infant have been reported. We experienced one case of the torsion of term pregnant uterus and report this case with a brief review of the concerned literature.
Axis, Cervical Vertebra ; Diagnosis ; Female ; Fetus* ; Humans ; Infant ; Mortality ; Mothers ; Myoma ; Ovarian Cysts ; Pregnancy ; Uterus*

The malignant mixed mullerian tumor (MMMT) is an uncommon tumor containing epithelial and mesenchymal components. MMMT of the ovary is rare, constituting less than 1% of all primary ovarian tumors. It is a particularly aggressive and rapidly progressive tumor, especially in advanced stages. This disease is usually advanced when diagnosed, because it is asymptomatic in early stage. The survival rate is very low in spite of surgery, chemotherapy and radiotherapy. The optimal treatment for this neoplasm is still controversial because of its rarity. We experienced one case of malignant mixed mullerian tumor of the ovary and report with a brief review of literature.
Drug Therapy ; Female ; Ovary* ; Radiotherapy ; Survival Rate

Dysgenetic streak gonads were removed laparoscopically from a phenotypic female with Swyer syndrome(ie, XY karyotype, sexual infantalism, primary amenorrhea, and Mullerian structures). Pathologic examination revealed a dysgerminoma in one of her gonads. We report a case of dysgerminoma with 46,XY Swyer syndrome and review of literature.
Amenorrhea ; Dysgerminoma* ; Female ; Gonadal Dysgenesis, 46,XY* ; Gonads ; Humans ; Infant ; Karyotype

Diabetic ketoacidosis (DKA) is an acute complication related to severe hyperglycemia. While the mortality rate for DKA is low with appropriate therapy, several complications may lead to deterioration of the clinical course. Here, we report a case of a 23-year-old patient with DKA who suffered from a rare but hemodynamically unstable cardiac arrhythmia, polymorphic ventricular tachycardia with prolonged QT interval, or Torsades de Pointes. During the recovery phase of DKA, three episodes of Torsades de Pointes suddenly occurred, and were recovered by immediate defibrillation. The patient did not have structural heart disease or a genetic predisposition. To the best of our knowledge, this is the first report of an adult with DKA complicated with QT prolongation related to Torsades de Points after correction of ketosis. To manage DKA, more attention may be needed on changes in the QT interval as well as risk factors for Torsades de Points.

Pseudomyxoma peritonei is a poorly understood condition characterized by gelatinous, mucinous implants, and often massive gelatinous ascites. It is commonly associated with mucinous tumors of the ovary or appendix, and a frequently relapsing and protracted disease. But, there are much confusion about its etiology, clinical manifestation, treatment, and prognosis. We experienced a case of pseudomyxoma peritonei originating from the borderline and microinvasive mucinous tumor of the ovary. So we report this case with a brief review of literatures.
Appendix ; Female ; Gelatin ; Mucins ; Ovary ; Prognosis ; Pseudomyxoma Peritonei*

Adenoma malignum (minimal deviation adenocarcinoma) is a rare, extremely well-differentiated form of invasive cervical adenocarcinoma. The name derives from the deceptively benign epithelial cells that line the glands of this neoplasm. The presence of architectural disorder with irregular, abnormally shaped invasive glands sometimes surrounded by a desmoplastic stromal response or demonstrating vascular and perineural invasion may be the only features establishing its malignant nature. Despite its bland appearance, adenoma malignum may carry a poor prognosis. Because of its rarity, and possibly because diagnostic changes are subtle and may be missed, there are few reports. A case of adenoma malignum of the uterine cervix is presented with a brief review of the literatures.
Adenocarcinoma ; Adenoma* ; Cervix Uteri* ; Epithelial Cells ; Female ; Prognosis

Adenoma malignum (minimal deviation adenocarcinoma) is a rare, extremely well-differentiated form of invasive cervical adenocarcinoma. The name derives from the deceptively benign epithelial cells that line the glands of this neoplasm. The presence of architectural disorder with irregular, abnormally shaped invasive glands sometimes surrounded by a desmoplastic stromal response or demonstrating vascular and perineural invasion may be the only features establishing its malignant nature. Despite its bland appearance, adenoma malignum may carry a poor prognosis. Because of its rarity, and possibly because diagnostic changes are subtle and may be missed, there are few reports. A case of adenoma malignum of the uterine cervix is presented with a brief review of the literatures.
Adenocarcinoma ; Adenoma* ; Cervix Uteri* ; Epithelial Cells ; Female ; Prognosis

The pathogenesis and origin of vulvar cyst lined by a ciliated columnar epithelium is unknown. But it is suggested that origins of the epithelium of cyst are Mullerian or Wolffian duct or urogenital sinus, while heterotopia (sequestration and migration of tissue) or dysontogenesis (defective embryonic development) or prosoplasia (abnormal development resulting in a "higher state" of organization) or metaplasia have also been suggested. We experienced one case of Mullerian cyst of vulva. So we report above the case with a brief review of literature.
Epithelium ; Metaplasia ; Vulva* ; Wolffian Ducts

The pathogenesis and origin of vulvar cyst lined by a ciliated columnar epithelium is unknown. But it is suggested that origins of the epithelium of cyst are Mullerian or Wolffian duct or urogenital sinus, while heterotopia (sequestration and migration of tissue) or dysontogenesis (defective embryonic development) or prosoplasia (abnormal development resulting in a "higher state" of organization) or metaplasia have also been suggested. We experienced one case of Mullerian cyst of vulva. So we report above the case with a brief review of literature.
Epithelium ; Metaplasia ; Vulva* ; Wolffian Ducts