Congenital pulmonary lymphangiectasis is a rare cause of severe respiratory distress in the newborn period and most of these patient die, usually within the first 24 hours of life. The light microscopic characteristics of the lungs are a network of partly tubular, partly cystically enlarged lymph vessels within large areas of connective tissue and they have thin wall lined by endothelium. Also congenital pulmonary lymphangiectasis is closely associated with cardiovascular malformation, and most frequently occurs in the clinical setting of congenital heart disease with or without pulmonary venous obstruction(total anomalous venous return, atresia of large pulmonary veins) The authors describe three typical cases of congenital pulmonary lymphangiectasis.
Connective Tissue ; Endothelium ; Heart Defects, Congenital ; Humans ; Infant, Newborn ; Lung ; Lymphangiectasis* ; Lymphangioleiomyomatosis

Hand tumorsare many and varied, although benign tumors are common. The pathology and histology of these tumors are not unlike these characteristics of the tumor when it occurs elsewhere. Early diagnosis and proper treatment of all hand tumors have been emphasized since the growth of tumors and pain can cause disturbance of intrinsic function of the hand. For the period of 10 years from 1977 to 1986, 105 cases of hand tumor were treated surgically and the results of clinical observation were as follows ; l. Among 105 cases, benign tumor was 101 cases(96.2%) Bone origin tumor was 20 cases, in which enchondroma and enchondromatosis were 17 cases(70%). Soft tissue origin tumor was 85 cases, in which ganglion was 54 cases(63.5%). 2. Among 105 cases, 42 cases were male and 63 cases were female. In age distribution, it showed even distribution. 3. In the duration of wymptom, 51 cases were below 1 year(48.6%). 4. The tumor occured 85 cases in soft tissue, 14 in phalanx, 7 in metacarpal and 1 in carpal bone. 5. The tumors were treated by excision or curettage and bone graft with good improvement, but postoperatively recurred in 2 cases of Hemangioma. Ampuation was performed in 3 cases of malignant tumors without recurrence.
Age Distribution ; Carpal Bones ; Chondroma ; Clinical Study ; Curettage ; Early Diagnosis ; Enchondromatosis ; Female ; Ganglion Cysts ; Hand ; Hemangioma ; Humans ; Male ; Pathology ; Recurrence ; Transplants

No abstract available.
Bone Density*

Arrhythmogenic right ventricular dysplasia/cardiomyopathy (ARVD/C) is characterized histologically by massive infilteration of right ventricular wall by fat tissue with surviving strands of cardiomyocytes bordered by or embedded in fibrosis. ARVC has been recognized as a cause of sudden death, especially in the young. We report an autopy case of ARVD/C in a 35-year-old female. She was found dead in her house under apparently natural circumstances. The autopsy revealed a dilated 340-gram heart with a fibrofatty replacement of the right ventricular myocardium. On the review of her past medical history, she had taken medical examination for prolonged general weakness about 1 year prior to death. At that time the echocardiogram revealed dilatation of right ventricular cavity size and moderately decreased left ventricular systolic function, the electrocardiogram revealed R>S at V1 lead and T-wave inversion at V1-V3 leads. To the best of our knowledge, this is the second autopsy case of ARVD/C, reported in the literature of Korea.
Adult ; Autopsy* ; Death, Sudden ; Dilatation ; Electrocardiography ; Female ; Fibrosis ; Heart ; Humans ; Korea ; Myocardium ; Myocytes, Cardiac

No abstract available.

No abstract available.
Peripheral Vascular Diseases*

The studies about tibial spine fracture were less frequently reported, especially in its sdult type, had different opinions according to authors. Meyers and McKeever described it had frequedntly occured as isolated injury without associated ligamentous injury of the same knee in children and mainly caused by bicycle accident. They had classified it by three different types according to the shape of it, managed conservatively type I, II,IIIA, and recommanded simple suturing with absorbable materials as operative method. But, in our cases it had frequently occured in adult and combined with ligamentous injury at the same knee including ACL and MCL. Also, it had frequently been caused by major trauma such as traffic accident. Previous method of management including simple stainless steel wiring had scored poor results in these complicated fractures. The author reviewed 24 cases of the tibial spine fracture treated at the Department of Orthopaedic Surgery, National Medical Center from June, 1980, to June, 1988, and the following results were obtained. 1. The most common causes of the injury were traffic accident (12 cases) and associated with rupture of medial collateral ligament in 7 cases. 2. The fracture was classified as four different types according to its pattern and comminution and most commen types were III and IV, scored 8 cases and 7 cases irrespectively. 3. Initially, closed sreduction and cast immobilization was performed in 15 cases, of which 8 cases had poor results with non-union of the fracture and instability. 4. Simple stainless steel wiring in 2 cases scored poor results and distal advancement of ACL with double wiring revealed good results in these cases. 5. One case of type II fracture had persistently positive anterior drawer sign and subjective instability and needed distal advancement of ACL and double wiring. 6. Distal advancement of ACL and double wiring was performed in 6 cases of which 4 cases revealed excellent results and 2 cases did good ones.
Accidents, Traffic ; Adult ; Child ; Classification ; Collateral Ligaments ; Humans ; Immobilization ; Knee ; Ligaments ; Methods ; Rupture ; Spine ; Stainless Steel

Sebaceous adenoma is a rare solitary or multiple yellow, circumscribed neoplasm consisting of sharply demarcated, proliferating lobules or irregular size and shape that are composed of three cell bypes: basal cells, mature and transitional sebaceous cells. We reported a case of extremely rare sebaceous adenoma arising in caruncle of the left eye in a 78-year-old female. A polypoid tumor nodule, measuring 0.6x0.5 cm, was noticed 6 months before resection. It was grayish white with granular surface. There is no evidence of associated visceral neoplasm. Histopathologically, it revealed a lobulated tumor, composed of equal amount of highly differentiated sebaceous and intermediate transitional epithelium with minor participation of basaloid cells. This tumor is thought to be the neoplasm of the sebaceous gland normaly present in the caruncle of the eye rather than ectopic origin.
Female ; Humans ; Adenoma

Meningiomas is the usually slow-growing lesions that present either with vague nonlocalizing symptoms or with focal findings referable to compression of underlying brain. Cerebral infarction by meningiomas is unusual, especially as the initial presentation in a patient, and association with sudden death is extremely rare. The authors report the clinical, radiological and pathological findings in a case of cerebral infarction caused by thrombosis of the right middle cerebral artery following direct compression of a right temporal lobe meningioma. A 48-year-old woman developed a history of sudden neurologic deterioration, and shortly after she died. CT showed a large cerebral infarction in the right lobe. Autopsy revealed a right temporal lobe meningioma associated with right middle cerebral artery thrombosis, which made a large cerebral infarction.
Autopsy ; Brain ; Cerebral Infarction ; Death, Sudden ; Female ; Humans ; Infarction, Middle Cerebral Artery ; Meningioma* ; Middle Aged ; Middle Cerebral Artery ; Temporal Lobe ; Thrombosis

Chronic rheumatic heart disease is the most important consequence of rheumatic fever and characterized principally by deforming fibrotic valvular disease(particularly mitral stenosis), which can produce permanent dysfunction and severe, sometimes fatal, cardiac dysfunction decades later. So the operation should be carried out in symptomatic patients with moderate to severe mitral or aortic stenosis or regurgitation. Postoperative mortality rate is low. But some postoperative complications including thromboembolism and prosthetic valve endocarditis are associated with high mortality. We report a autopsy case diagnosed as cerebral infarction due to thromboembolic complication of rheumatic heart disease patient with mechanical mitral and aortic prostheses. To our knowledge, this is the initial autopsy presentation of cerebral infarction due to thromboembolic complication of mechanical prosthetic valve in the patient with rheumatic heart disease in Korea.
Aortic Valve Stenosis ; Autopsy ; Cerebral Infarction* ; Endocarditis ; Heart Valve Prosthesis ; Humans ; Korea ; Mortality ; Postoperative Complications ; Prostheses and Implants* ; Rheumatic Fever ; Rheumatic Heart Disease* ; Thromboembolism