Cutis laxa is a rarely discussed entity which manifests itself primarily as loose redundant skin and may be accompanied by internal anomalies. Localized cutis laxa is involved to the ear lobules, eyelids an lips in 34 years old male was described. Diagnosis of localized cutis laxa was established by clinical characteristic manifestations and histopathological studies.
Adult ; Cutis Laxa* ; Diagnosis ; Ear ; Eyelids ; Humans ; Lip ; Male ; Skin

Frorn August to December 1973, 189 cases of scabies were examinecl by Muller's method and following results were obtained: 1) 91 cases (52. 6%) of 172 were confirmed by detecting mite. 2) From the reexamination of samples, adult form(58.2%), larva(52.7%), egg(41.8%), egg shell(30.8%) and scybala(29.7%) were identified in order and egg shell and scybala were also diagnostic. 3) Confirmed scraping lesions were burrow(61. 8%),papule(29.4%), vesicle(5.9%) pustule(2.9%), in order of frequency. 4) Adult Sarcoptes was found in 27 cases(64.3%) of 42 examined with burrows and in 13 cases(65%) of 20 with papules. 5) Mean of incubation period was 26.6 days in 14 cases.
Adult ; Animals ; Egg Shell ; Humans ; Mineral Oil* ; Mites ; Ovum ; Scabies*

No abstract available.
Humans ; Tuberculosis, Pulmonary*

No abstract available.
Humans ; Siblings* ; Thrombasthenia*

No Abstract available.
Transcription Factors*

Moyamoya is a chronic cerebrovascular disease characterized by progressive stenosis or occlusion of the terminal parts of both intermal carotid arteries with telangiectatic vascular network of collateral circulation at the base of the brain and leptomeningeal arteries. The etiology and pathophysiology of this disease are still unknown. Although the idiopathic presentattion is the commonest, moyamoya disease has also been reported in several hereditary or acquired clinical conditions including neurofibromatosis, sickle cell anemia, tuberculous meningitis, atherosclerosis, and following radiation therapy to the head. The term moyamoya disease should be reserved for those cases in which the characteristic angiogrphic pattern is idiopathic; moyamoya syndrome is used when the underlying condition is known. We have experienced a case of coexistence of moyamoya syndrome and hereditary spherocytosis in a 6-year-8-month-old girl who presented with right-sided hemiparesis and pallor. A cerebral angiogram revealed occlusion of proximal portion of left middle cerebral artery and abnormal collateral network. The peripheral blood smear and osmotic fragility test disclosed hereditary spherocytosis. To our knowledge, the coexistence of moyamoya syndrome and hereditary spherocytosis has not been documented. We report here the case and the brief review of related literatures. Further studies are needed to clarify the intimate relationship between the two diseases.
Anemia, Sickle Cell ; Arteries ; Atherosclerosis ; Brain ; Carotid Arteries ; Collateral Circulation ; Constriction, Pathologic ; Female ; Head ; Humans ; Middle Cerebral Artery ; Moyamoya Disease* ; Neurofibromatoses ; Osmotic Fragility ; Pallor ; Paresis ; Tuberculosis, Meningeal

Visible light can induce damage to the susceptible retina and its injurious effect has been studied morphologically and functionally in detail. In order to evaluate the regenerative processes of the retina damaged by visible light in correlation with the degree of the cellular damage, the rat retina was exposed to blue visible light (400-500nm) for 30, 60 and 120 minutes, and examined electron microscopically, immediately and 1, 2, 3, 4, 5 weeks after the exposure. The results were as follows. The more increased time of exposure by visible light, the more damage to the photoreceptor, and the more delay in the recovery. We observed the recovery of damage was generally slow, and the pigment epithelium necessary for regeneration of discs was not destroyed in spite of long term exposure of visible light.
Animals ; Epithelium ; Light ; Rats ; Regeneration ; Retina

No Abstract Available.
Intercellular Signaling Peptides and Proteins* ; Polyethylene*

No abstract available.
Heart Atria*

The major pathogenesis of acute respiratory distress syndrome (ARDS) is an inflammatory process that results from a diversity of injuries to the body. Due to the various cytokines and vasoactive peptides released from the endothelium, the vascular permeability is increased; the migration of inflammatory cells and the leakage of plasma proteins then occur and edema develops in the alveolus. There is a hypothesis that the impairment of alveolar recruitment in ARDS is caused by a defect of the surfactant system and the resultant increase of alveolar surface tension. This has been studied in pediatric patients in ARDS; after the administration of surfactant, hypoxia, respiratory symptoms and survival chances were improved. To alleviate the major pathogenic mechanism in this disease, that is to say, inflammation of the lung, steroids have been used and studied as another treatment modality for ARDS, and it has been concluded that the administration of low dose methylprednisolone may improve patients' symptoms and survival rates. We report here on a case of a young infant admitted with ARDS, who, after the intratracheal administration of 120 mg/kg surfactant, on PaO(2)/FiO(2) was elevated. Subsequent low doses of methylprednisolone were given, and the symptoms did not recur, and no fibrotic change was shown during the follow-up period of 2 months.
Anoxia ; Blood Proteins ; Capillary Permeability ; Cytokines ; Edema ; Endothelium ; Follow-Up Studies ; Humans ; Infant ; Inflammation ; Lung ; Methylprednisolone* ; Peptides ; Respiratory Distress Syndrome, Adult* ; Steroids ; Surface Tension ; Survival Rate