1.Melanotic Neuroectodermal Tumor of Infancy in the Epididymis: A Case Report.
Sang Bae LEE ; Seong Hun LEE ; Min Hyuk RYU ; Ji Seoung PARK ; Joo Heoun YANG ; Sun Young KIM ; Dong Jean LEE
Korean Journal of Pediatrics 2004;47(12):1334-1337
Melanotic neuroectodermal tumor of infancy (MNTI) is a rare neoplasm known by a variety of names including melanotic progonoma and retinal anlage tumor, and currently thought to be neural crest derivation. The vast majority develop within the first year of life. The behavior is generally benign, but recurrent and metastatic cases have been documented. It arises in the head and neck in over 90%, mainly in the maxilla, but is extremely rare in the epididymis. We report a case of MNTI together with a review of literature, which occurred in the right epididymis of a 6-month-old boy who presented with a painless, slowly growing, scrotal mass and was treated with radical orchiectomy.
Epididymis*
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Head
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Humans
;
Infant
;
Male
;
Maxilla
;
Neck
;
Neural Crest
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Neuroectodermal Tumor, Melanotic*
;
Orchiectomy
2.Multiple Rhabomyomas in left Ventricular Outflow Tract Combined with Tuberous Sclerosis: A Case Report.
Young Chul YOON ; Kwang Hyun CHO ; Keoung Heoun KIM ; Hee Jae JUN ; Kang Joo CHOI ; Yang Jaeng LEE ; Youn Ho HWANG
The Korean Journal of Thoracic and Cardiovascular Surgery 2002;35(10):745-749
Cardiac rhabdomyoma is a rare type of benign tumor affecting the heart. There are a few previous reports of intracardiac rhabdomyomas causing ventricular arrythmia. We describe a 1-year-old female tuberous sclerosis patient who was presented with a ventricular tachycardia. Diagnostic echocardiography revealed two masses in the left ventricular outflow tract originating from the ventricular septum. The masses were surgically resected through aortotomy using cardiopulmonary bypass and the masses appeared benign. The pathology was that of a cardiac rhabdomyomas. Postoperative course was uneventful and the ventricular tachycardia was controlled.
Arrhythmias, Cardiac
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Cardiopulmonary Bypass
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Echocardiography
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Female
;
Heart
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Heart Neoplasms
;
Humans
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Pathology
;
Rhabdomyoma
;
Tachycardia, Ventricular
;
Tuberous Sclerosis*
;
Ventricular Septum