No abstract available.
Encephalitis, Arbovirus* ; Prognosis*

No abstract available.
Polycystic Kidney Diseases*

Xeroderma pigmentosum is characterized by sunlight sensitivity, autosomal recessive inheritance, and multiple cutaneous malignant melanoma, angiosarcoma and fibrosarcoma. Some patient also demonstrate neurological manifestations, ie, mental deficiency, microcephaly, ataxia, choreoathetosis, and deafness. A 22 year old Korean soldier was seen at the Capital Armed Forces General Hospital in May of 1974 because of pigmentation and ulceration on the exposed area. Since the age of 3, the patient has suffered from freckles on exposed area and the lesions were gradually increased in number. About 3 years ago, he observed nodule on the left side of face, which underwent ulceration eventually. There were no history of unconsciousness, convulsion or other neurological symptoms. The histopathological picture in the margin of ulcerated lesion revealed hyperkeratosis and acanthosis in epidermis, and masses of various shaped and sized composed of basalioma cells in dermis. The peripheral cell layer of the tumor masses showed pallisade arrangement of the nuclei.
Arm ; Ataxia ; Deafness ; Dermis ; Epidermis ; Fibrosarcoma ; Hemangiosarcoma ; Hospitals, General ; Humans ; Ichthyosis* ; Intellectual Disability ; Melanoma ; Melanosis ; Microcephaly ; Military Personnel ; Neurologic Manifestations ; Pigmentation ; Seizures ; Sunlight ; Ulcer ; Unconsciousness ; Wills ; Xeroderma Pigmentosum* ; Young Adult

The Becker's nevus (pigmentary hairy edidermal nevus) is a variety of epidermal nevus in which epidermal thickening may be minimal, and hairiness and pigmentation obvious. Characteristically it is a unilateral lesion of the shoulder in males but it may affect other sites, be multiple and bilateral, and be found in women and negroes. Histologically nevus cells are not seen in the dermis. A man aged 25 had the nevus covering extensive area on his right shoulder since 2 years ago. The pigmentation was dark brownish and hairy. The pigmented area was noninfiltrated and in place showed perifollicular darkening. Coarse hairs were noticed since a year. ago. The histopathological picture showed hyperkeratosis, acanthosis, papillomatosis and increased melanin pigments in the basal cell layer. Nevus cells were not seen in the dermis.
African Continental Ancestry Group ; Dermis ; Female ; Hair ; Humans ; Male ; Melanins ; Nevus* ; Papilloma ; Pigmentation ; Shoulder

A 48-year-old woman, who had had tattoo on her eyebrows, was seen with pruitic erythematous indurated plaques on the tattooing sites. The skin react ion was begun to observe about 4 weeks after getting tattoo. Skin biopsy specimens from the indurated lesions showed granulomatous reactions. Intradermal tests by means of multiple pricks and patch test were done on her low back with the same tattoo dye and also 4 others available in Korea. Serial punch biopsy specimens were obtained from the sites of intradermal test at 2nd, 7th, 28th, and 56th day after intradermal test. Granulomatous reactions were found in the spiecimens taken at the 28th and 56th day.
Biopsy ; Eyebrows ; Female ; Humans ; Intradermal Tests ; Korea ; Middle Aged ; Patch Tests ; Skin ; Tattooing

No abstract available.
Bronchiolitis* ; Respiratory Sounds*

No abstract available.
Esophageal Atresia* ; Tracheoesophageal Fistula*

Sjogren-Larsson Syndrome is a rare disorder chracterized by congenital icthyosis, spastic diplegia or tetraplegia and mental retardation. The inheritance is autosomal recessive, due to deficiency of alcohol dehydrogenase activity of fatty acid matabolism. We have experienced a case of Sjogren-Larsson Syndrome in a 16 month-old male children who have dried thick skin, developmental delay, and spastic diplegia. He also has glistening spot on macula area with irregular high voltage slow wave (2-3Hz) on electroencephalography. From Biopsy finding, Lamella ictyosis with acanthosis and hyperkeratosis in epithelium is shown. He was much improved clinically for skin lesion and developmental status with etretinate supplement. We report the case with brief review of related literatures.
Acitretin ; Alcohol Dehydrogenase ; Biopsy ; Cerebral Palsy ; Child ; Electroencephalography ; Epithelium ; Etretinate ; Humans ; Infant ; Intellectual Disability ; Male ; Quadriplegia ; Sjogren-Larsson Syndrome* ; Skin ; Wills

No abstract available.
Antigen-Antibody Complex* ; Syphilis*

No abstract available.
Bilirubin* ; Humans ; Infant, Newborn*