1.A Case of Congenital Intrahepatic Portosystemic Shunt Associated with VSD Detected by Antenatal Sonography and Treated with Four Coil Embolizations and Open Heart Surgery after Birth.
Ji Youn NA ; Eun Sun KIM ; Sang Duk KIM ; Ee Kyung KIM ; Han Suk KIM ; Jung Hwan CHOI ; Jeong Eun CHUNG ; Jin Uuk JOUNG
Journal of the Korean Society of Neonatology 2008;15(2):176-182
A congenital portosystemic shunt is a very rare portosystemic vascular anomaly which leads to jaundice, hypoglycemia, hyperammonemia, liver cirrhosis, hepatic coma, and pulmonary hypertension. Anatomically, portosystemic shunts are divided into intra- and extra- hepatic shunts. Congenital intrahepatic portosystemic shunts are rare anomalies, and the early diagnosis is important to prevent hepatic encephalopathy and hypoglycemia. We report a case of an infant with symptoms of heart failure due to a congenital intrahepatic portosystemic shunt and a ventricular septal defect (VSD), which were treated successfully with four coil embolizations and open heart surgery for the VSD.
Early Diagnosis
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Heart
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Heart Failure
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Heart Septal Defects, Ventricular
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Hepatic Encephalopathy
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Humans
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Hyperammonemia
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Hypertension, Pulmonary
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Hypoglycemia
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Infant
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Jaundice
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Liver Cirrhosis
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Parturition
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Portasystemic Shunt, Surgical
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Thoracic Surgery