Lymphangioma circumscriptum was known as very rare disorder in our country. The patient was 28 year old man had been affected grouped papulovesicular lesion on right arm without subjective complaint. Histopathological finding shows in the upper most portion of the dermis cystically dilated lymph vessels lined by a single layer of endothelium. They contain coagulated lymph and lymphocytes. Over some of the lymph cyst it is thinned, elswhere it may show focal acanthosis, hyperkeratosis.
Adult ; Arm ; Dermis ; Endothelium ; Humans ; Lymphangioma* ; Lymphocytes

Incomplete fixation of pancreas, which may be associated with a wide mobility of root of SMA, result in chronic midgut volvulus. Movable pancreas is an uncommon form of incomplete intestnal fixation and rotation. Herein, we present a caae of movable pancreas. A patient was a 32-year-old male with the complaint of colicky intermittent abdomnal pain. The abdominal ultrasonography and CT showed a movable pancreas. The head of pancreas was located in the left of the abdominal aorta during the inspiratory time and left decubitus position. At surgery, pancreas was mobile and the root of mesentery was very weak and fibrotic. Duodenum and mesentery were fixed by 0.7 mm Dacron patch along the right peritoneal gutter and the retroperitoneum from ligament of Treitz to the ileocecal attachment. Duodenojejunostomy was performed for the prevention of SMA syndrome. The symptoms disappeared and recovery was prompt. Following the procedure, the patient remains asymptomatic until 10 months after operation
Adult ; Aorta, Abdominal ; Duodenum ; Head ; Humans ; Intestinal Volvulus* ; Ligaments ; Male ; Mesentery ; Pancreas* ; Polyethylene Terephthalates ; Ultrasonography

Two cases of leukemia cutis associated with leukemia has been demonstrated. Case 1: 24 year old man had been fever, arthralgia and leproma like hard infiltrated nodular lesion with hemorrhagic macules was noted on face and upper arms and trunk, Monocytic Jeukemia has been presented. In peripheral blood and bone marrow finding, immature blood cells was counted in about 80%, Case 2: 64 yearold woman, had been erythematous papule with itching on lower extremities and coin ized ulcerated nodule was noted on lumbosacral region. Myeloid leukemia has been presented. In peripheral blood and bone marrow finding, immature blood cells was counted in about 7.2%. Diagnosis of cutaneous lesions was by clinical apperance and histopathological change. By laboratory examination, monocytic leukemia and myeloid leukemia was revealed in peripheral blood and bone marrow preparation.
Arm ; Arthralgia ; Blood Cells ; Bone Marrow ; Diagnosis ; Female ; Fever ; Humans ; Leukemia* ; Leukemia, Myeloid ; Lower Extremity ; Lumbosacral Region ; Numismatics ; Pruritus ; Ulcer ; Young Adult

Obstructive jaundice of the bile duct resulting from tumor-producing copious, thick mucin, causing ductal obstruction and dilatation, has been reported very rarely. Also, the benign bile duct neoplasm is extremely rare. We report a case of a mucin-secreting villous adenoma of common hepatic duct causing obstructive jaundice and cholangitis. The patient was a 72-year-old male and had a 3 yeared history of common hepatic mass unchanged remarkably in size. The abdominal ultrasonogram and computed tomography revealed well circumscribed, more than 2cm sized mass on the CHD and ductal dilatation. We were able to get an interesting cholangioram showing irregular, nodular, ill defined filling defect in the extrahepatic bile duct, different from US and CT findings, And it was just caused by thick, copious mucin from the tumar. This case was confirmed as mucin-secreting villous adenoma after surgery.
Adenoma, Villous* ; Aged ; Bile Duct Neoplasms ; Bile Ducts ; Bile Ducts, Extrahepatic ; Cholangitis ; Dilatation ; Hepatic Duct, Common* ; Humans ; Jaundice, Obstructive ; Male ; Mucins* ; Ultrasonography

A case of lichen nitidus in 23 years old male was described. This is the first case report in Korea. The clinical and histopathological study revealed characteristic features of the disease. Authors reviewed therapeutic experience and reports of the literaturea.
Humans ; Korea ; Lichen Nitidus* ; Lichens* ; Male ; Young Adult

No abstract available.
Heart Valves* ; Heart*

Sjögren-Larsson syndrome(SLS) is a rare hereditable disease characterized by congenital ichthyosis, spastic diplegia and mental retardation. Along with the typical triad of symptoms, many patients with this disease have short stature, kyphosis and glistening dots in the retina of the eye. The pathogenesism is unknown but recent studies suggest that SLS might be, at least in part, a disorder of fatty acid metabolism. We describe a patient with a pathognomonic finding in the fundus and with the classic features of SLS.
Cerebral Palsy ; Humans ; Ichthyosis ; Intellectual Disability ; Kyphosis ; Metabolism ; Retina ; Sjogren-Larsson Syndrome*

No abstract available.

Steatocystoma multiplex is a relatively rare condition characterized by multiple, small, yellowish, cystic nodules 2 to 4mm in diameter locatcd princioally on the upper arms and the thighs. This has a high familial tendency and probably has an autosomal dominant mode of transmission. These tumors of steatocystoma multiplex characteristically contain hair follicles and sebaceous glands, and are to be the dermoid cyst. There was a familial and congenital inferiority in the ectoderm in both patient and family, ie, ichthyosis, hypohidrosis, koilonychia, milia and comedones. A 26 year-old Korean soldier was seen in February of 1970. His condition started 10 years previously. The widespread cystic nodules were 0. 2 to 1 cm in size and yellowish in color, and located on chest, back, scrotum and behind both ear lobes. There was thickening and daky brownish discolorations of all finger and toe nails. His father and two brothers had similar disorders, HistoIogieally clusters of hairs, mainly of lanugo size but some of intermediate character, were found in the lumen.
Adult ; Arm ; Dermoid Cyst ; Ear ; Ectoderm ; Fathers ; Fingers ; Hair ; Hair Follicle ; Humans ; Hypohidrosis ; Ichthyosis ; Military Personnel ; Scrotum ; Sebaceous Glands ; Siblings ; Steatocystoma Multiplex ; Thigh ; Thorax ; Toes

No abstract available.
Heart Atria* ; Histiocytoma, Malignant Fibrous*