A 12-year-old boy was referred to our ENT clinic with an incidentally discovered left supraclavicular mass that was suspected to be malignant. He was asymptomatic and had no prior illnesses. Neck examination found a fixed, hard, non-pulsatile, and non-tender mass measuring 2 cm in diameter in the left supraclavicular fossa. Rest of the ENT assessment, chest and upper limb neurovascular examinations were unremarkable. The patient’s full blood count was within the normal range.

Temporal bone rhabdomyosarcoma is an aggressive entity that simulates chronic otitis ear infection. It is the most common soft tissue sarcoma amongst pediatric patients. Herein, we would like to report a case of temporal bone rhabdomyosarcoma involving a 2-year-old boy who presented with a one-month history of otorrhea with facial asymmetry. Early treatment led to remission of this severe neoplasm