We report the FDG PET findings in a patient with Marchiafava-Bignami disease (MBD) in whom there was diffusely reduced metabolism in the whole brain cortex and strongly decreased metabolism in the thalami. The use of FDG PET helps provide an understanding of the neurologic manifestations and prognosis of MBD.
Alcoholism ; Brain ; Humans ; Marchiafava-Bignami Disease* ; Metabolism ; Neurologic Manifestations ; Prognosis

Osteopathia Striata is a rare developmental abnormality characterized by striation of the skeleton, especially the metaphyses of the long bones. It has been seen on only a few occasions since it was first described by Voorhoeve in 1924. This case, a nine year old boy, showed well marked striation throughout bones of right lower extremity and pelvis and so justifies the title of paper.
Humans ; Lower Extremity ; Male ; Pelvis ; Skeleton

Congenital clasped thumb is an unusal condition characterized by the thumb being held tightly beneath the flexed fingers in such a way that it cannot escape for normal prehension. New-born infants frequently hold their thumbs beneath their flexed fingers. If the flexed thumb persists and normal independent action of the thumb does not develop third or fourth month after birth, congenital clasped thumb is suggested. It is the result of failure of normal developmenl of the muscles and tendinous structures that provide extension for the thumb and fingers at the metacarpophalangeal joint. The deformity also includes volar soft tissue contractures of digits in varying degrees of severity. Since first description of Zadek in 1934 for bilateral thumb extensor agenesis. total 48 cases of congenital clasped thumb have been reparted throughout the world. A case of bilateral congenital clasped thumb with bilateral calcaneo-varus deformity in one month-old boy was diagnosed and treatment with prospect of complete funtional recovery.
Congenital Abnormalities ; Contracture ; Fingers ; Humans ; Infant ; Male ; Metacarpophalangeal Joint ; Muscles ; Parturition ; Thumb ; United Nations

Slipped femoral capital epiphysis is the condition in which the femoral head begins to slip gradually off the femoral neck. After first discription of Ambrose Pare(1572), the world literature has presented many cases, usually more than one hundred in each clinic. Its incidence in Korea, however, is extremely rare and particularly it is difficult to find out the report of typical case. The author reports here a typical case of billateral slipped femoral capital epiphysis in a 17 year old boy with symptom duration of 2 years on right side and 6 months on left side. Physical examination showed his body stature to be normal and his genital organs to have no abnormalities. However, both hips revealed severe pain and limited range of motion, especially in internal rotation and abduction, which restricted his normal gait. Operative reduction of epiphysio-cervical distorsion was successful in the left hip. After skeletal traction of the left hip, an anatomical repositioning by intraarticular wedge rection osteotomy was maintained by 3 Knowles pins. 3 months postoperatively he resumed partial weight bearing on his left hip with little pain and improved range of motion. Further restoration of function can reasonably be expected.
Epiphyses ; Femur Neck ; Gait ; Genitalia ; Head ; Hip ; Humans ; Incidence ; Korea ; Male ; Osteotomy ; Physical Examination ; Range of Motion, Articular ; Traction ; Weight-Bearing

No abstract available.
Mortality* ; Tooth Loss* ; Tooth*

No abstract available.
Gallstones*

To our knowledge, rectal cancer arising at the anastomotic site after surgery for Hirschsprung's disease has not been reported. We report a case of mucinous adenocarcinoma arising at the anastomotic site after Soave operation 26 years ago.
Adenocarcinoma, Mucinous* ; Hirschsprung Disease* ; Mucins* ; Rectal Neoplasms

The treatment of extensive soft tissue injury is a chsllenge to Orthopedidic Surgeon especially in young children and at present reconstructive surgery with free flap is being employed under microscopy actively. The author present 27 cases of free flaps in young children below 6 years old, which were performed from March 1983 to December 1986. The results are as followes ; 1. The mean age was 4.9 years old. 2. The mechanism of injuries were all pedestrian injury. 3. We performed 27 cases of free flaps, among them 24 cases of flap were survived(88.9 %) with good functional and cosmetic result. 4. The vessels were larger in these young children than we expected. It is apparent that in a healthy child even though below 6 years old, the careful application of microsurgical principle is an excellent method for salvaging devascularized parts that are vital for function or appearance.
Child ; Clinical Study ; Free Tissue Flaps ; Humans ; Methods ; Microscopy ; Soft Tissue Injuries

We report a case of kerion celsi caused by Trichophyton verrucosum in a 4-year-old male. He presented painful, tender, indurated, boggy masses discharing pus on the vertex and occiput. Kerion celsi caued by T. verrucosum was diagnosed by the characteristic gross and microscopic findings of the colony on the Sabourauds glucose. agar. The possible source of infection was searched and wq found that he raised the cattles in his house. They had multiple, scaly, whitish plaques on the skin and T. verrucosum was identified from the hairs of the lesions. He had been treated with griseofulvin and prednisolone, and all lesions were cleared leaving partial alopecia in 2 months.
Agar ; Alopecia ; Child, Preschool ; Glucose ; Griseofulvin ; Hair ; Humans ; Male ; Prednisolone ; Skin ; Suppuration ; Tinea Capitis* ; Trichophyton*

We describe a patient with overlap syndrome in whom systemic lupus erythematosus and scleroderma were combined. The patient expired due to severe central nervous system involvernent and pneumonia. Pertinent neuropsychiatric signs of the patient included generalied seizure, impairment of recent, memory, dysarthria, mental deterioration, Balints syndrome, right sided hemiparesis and right sided central type facial weakness. Hrain MRI and cerebral angiogram slowed cerebral vasculopathy. We suggest that a long-term follow-up is necessary for the confirmation of ciagnosis of a connective tissue disease, because the evolution, transition and overlapping features among the group of connective tissue diseases may commonly occur over time.
Central Nervous System ; Connective Tissue Diseases ; Dysarthria ; Follow-Up Studies ; Humans ; Lupus Erythematosus, Systemic ; Magnetic Resonance Imaging ; Memory ; Paresis ; Pneumonia ; Seizures