1.Valve Sparing Aortic Root Replacement in Children with Loeys-Dietz Syndrome.
Hyung Tae SIM ; Dong Ju SEO ; Jeong Jin YU ; Jae Suk BAEK ; Hyn Woo GOO ; Jeong Jun PARK
The Korean Journal of Thoracic and Cardiovascular Surgery 2015;48(4):272-276
Loeys-Dietz syndrome (LDS) is an autosomal dominant connective tissue disorder that is characterized by aggressive arterial and aortic disease, often involving the formation of aortic aneurysms. We describe the cases of two children with LDS who were diagnosed with aortic root aneurysms and successfully treated by valve-sparing aortic root replacement (VSRR) with a Valsalva graft. VSRR is a safe and suitable operation for children that avoids prosthetic valve replacement.
Aneurysm
;
Aorta
;
Aortic Aneurysm
;
Aortic Diseases
;
Child*
;
Connective Tissue
;
Humans
;
Loeys-Dietz Syndrome*
;
Transplants