4.A Case of Histiocytosis-X.
Jung Hyun CHO ; Byeong Wook HWANG ; Nam Hoon OH ; Su Il YOO ; Dal Sung HWANG ; In Sun HA ; Yong Sung LEE
Journal of Korean Neurosurgical Society 1994;23(12):1464-1469
The authors have experienced a case of histiocytosis-X. A 7-year-old male patient had three tender masses, one on the right parietal region, another on the left parietal region, the other on the left occipital region and revealed exophthalmus on his left side. Plain skull films showed multiple punched out skull defects and on lumbar spine films, collapse of body of second lumbar vertebra was detected. Among the masses, the largest right parietal one was excised totally. The final diagnosis revealed histiocytosis-X on pathologic basis and he was given subsequent chemotheraphy.
Child
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Diagnosis
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Histiocytosis, Langerhans-Cell*
;
Humans
;
Male
;
Rabeprazole
;
Skull
;
Spine
5.Langerhans Cell Histiocytosis with Pancreatic Involvement: Imaging Findings Including Diffusion-Weighted Imaging.
Jun Hwee KIM ; Myung Joon KIM ; Chuhl Joo LYU ; Mi Jung LEE
Journal of the Korean Society of Magnetic Resonance in Medicine 2012;16(3):262-265
Langerhans cell histiocytosis (LCH) can affect many different organs. However, LCH with pancreatic involvement is very rare with a few reports about imaging findings. We present a case of multisystemic LCH with pancreatic involvement in a five-week-old infant. Pancreas lesion showed hypoechoic on ultrasonography, low density with poor enhancement on CT, and restricted diffusion on diffusion-weighted imaging. Although LCH with pancreatic involvement is rare, LCH should be considered in the differential diagnosis of pancreatic mass in children.
Child
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Diagnosis, Differential
;
Diffusion
;
Histiocytosis, Langerhans-Cell
;
Humans
;
Infant
;
Pancreas
8.Langerhans cell histiocytosis in children with nasal congestion as chief complain: a case report.
Yuanding ZHANG ; Weilun CHEN ; Yining LI
Journal of Clinical Otorhinolaryngology Head and Neck Surgery 2015;29(24):2177-2179
Langerhans cell histiocytosis (LCH) is a rare histiocytic disorder. Here, we report a rare case of multi-system LCH in a 20-month-old children presenting nasal congestion, fever, abnormal liver function, anemia, and skin damage. The radiograph computed tomography showed an osteolytic lesion in the lateral skull base with tumor extension. Pathological biopsy was performed, and the histopathologic diagnosis was LCH. A general review of LCH, including clinical manifestations, diagnosis, treatment, and prgognosis, is presented.
Histiocytosis, Langerhans-Cell
;
diagnosis
;
Humans
;
Infant
;
Rare Diseases
9.Oral mucosal lesions with transient self-healing of Langerhans cell histiocytosis: a case report.
Xiaoling ZHANG ; Ningning XUE ; Minhui RUAN ; Xin ZENG
West China Journal of Stomatology 2023;41(5):592-598
Langerhans cell histiocytosis (LCH) is a group of unexplainable abnormal proliferation and aggregation of Langerhans cell. LCH can be classified into four clinical variants: Letterer-Siwe disease, Hand-Schüller-Christian disease, eosinophilic granuloma, and congenital self-healing LCH. LCH is most prevalent in children. Lesions can be localized in a single system or multiple organs, and clinical manifestations vary depending on the affected organs. The skin and mucocutaneous tissues are the starting point of the affected tissue. This study presents a LCH case characterized by transient self-healing. This case can further provide references for the clinical diagnosis and treatment of LCH.
Child
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Humans
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Histiocytosis, Langerhans-Cell/therapy*
;
Diagnosis, Differential
10.Rosai-Dorfman Disease as a Solitary Lesion of the Tibia.
Chang Bae KONG ; Jung Wook LEE ; Sang Hyun CHO ; Won Seok SONG ; Wan Hyeong CHO ; Jae Soo KOH ; Dae Geun JEON ; Soo Yong LEE
The Journal of the Korean Bone and Joint Tumor Society 2014;20(1):32-35
Rosai-Dorfman disease (RDD) is an idiopathic histioproliferative disorder of lymph node and extranodal site. Bone involvement is very rare. We report a case of extranodal RDD of the tibia in 32-year old male. The patient presented with pain with no evidence of lymphadenopathy. Clinico-radiologic diagnosis was metastatic carcinoma or Langerhans cell histiocytosis, but, histopathologic examination confirmed the diagnosis with RDD. We performed curettage on the osteolytic lesion of tibia. In South Korea, there was no report about RDD of the extremity and we want to report this case with review of the literature.
Curettage
;
Diagnosis
;
Extremities
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Histiocytosis, Langerhans-Cell
;
Histiocytosis, Sinus*
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Humans
;
Korea
;
Lymph Nodes
;
Lymphatic Diseases
;
Male
;
Tibia*