1.Caroli's Syndrome with Autosomal Recessive Polycystic Kidney Disease in a Two Month Old Infant.
Jeong Tae KIM ; Yoon Jeong HUR ; Jee Min PARK ; Myung Joon KIM ; Young Nyun PARK ; Jae Seung LEE
Yonsei Medical Journal 2006;47(1):131-134
Caroli's syndrome is a rare congenital disorder that involves intrahepatic bile duct ectasia and congenital hepatic fibrosis, frequently seen with concomitant autosomal recessive polycystic kidney disease (ARPKD). Literature on infants with ARPKD is rare. Here, we present a case of a two month old boy who was diagnosed with Caroli's syndrome and ARPKD.
Polycystic Kidney, Autosomal Recessive/complications/*diagnosis/pathology
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Male
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Kidney/ultrasonography
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Infant
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Humans
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Hepatic Duct, Common/pathology/ultrasonography
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Caroli Disease/complications/*diagnosis/pathology
2.Unilocular Extrahepatic Biliary Cystadenoma Mimicking Choledochal Cyst: A Case Report.
Ju Hyun PARK ; Dong Ho LEE ; Hyoung Jung KIM ; Young Tae KO ; Joo Won LIM ; Moon Ho YANG
Korean Journal of Radiology 2004;5(4):287-290
We report here on a case of extrahepatic biliary cystadenoma arising from the common hepatic duct. A 42-year-old woman was evaluated by us to find the cause of her jaundice. Ultrasonography and CT showed a cystic dilatation of the common hepatic duct and also marked dilatation of the intrahepatic duct. Direct cholangiography demonstrated a large filling defect between the left hepatic duct and the common hepatic duct; dilatation of the intrahepatic duct was also demonstrated. Following excision of the cystic mass, it was pathologically confirmed as a unilocular biliary mucinous cystadenoma arising from the common hepatic duct.
Adult
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Bile Duct Neoplasms/*diagnosis
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Cholangiopancreatography, Magnetic Resonance
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Choledochal Cyst/*diagnosis
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Cystadenoma/*diagnosis
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Diagnosis, Differential
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Female
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Hepatic Duct, Common/*pathology/radiography/ultrasonography
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Humans
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Tomography, X-Ray Computed
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Ultrasonography, Interventional