Hemangioendothelioma, Epithelioid ; pathology ; Humans

Hemangioendothelioma, Epithelioid ; pathology ; Humans ; Lung Neoplasms ; pathology

Hemangioendothelioma, Epithelioid ; diagnosis ; Humans ; Temporal Bone ; Vascular Neoplasms ; diagnosis

Intracranial epithelioid hemangioendothelioma is extremely rare. We report a case of intracranial epithelioid hemangioendothelioma which developed in a 55-year-old man who presented with dysarthria for two weeks. The brain computed tomography scan and magnetic resonance image showed masses which had fat component at the left frontal convexity and at left posterior parietal area. Excisional biopsy at the left frontal convexity confirmed epithelioid hemangioendothelioma which is immunopositive for CD31, supporting endothelial differentiation, and negative for CD68, SMA and HMB-45.
Biopsy ; Brain ; Dysarthria ; Hemangioendothelioma, Epithelioid* ; Humans ; Middle Aged ; Rabeprazole

Hepatic epithelioid hemangioendothelioma is a rare tumor of vascular origin having a intermediate clinical course between benign cavernous hemangioma and malignant anglosarcoma. Patients present nonspecific clinical signs and symptomas. We experienced a case of surgically proven hepatic epithelioid hemangioen-dothelioma. Computed tomography showed multiple nodules with internal calcifications, chiefly in peripheral portion of both lobes of the liver. Ultrasonography showed hypoechoic nodules and tiny calcific foci in peripheral portion. Open biopsy of the liver and the omenrum confirmed epithelioid hemangioendotheliomas.
Biopsy ; Hemangioendothelioma, Epithelioid* ; Hemangioma, Cavernous ; Humans ; Liver* ; Ultrasonography

Hemangioendothelioma, Epithelioid ; Humans ; Liver Neoplasms ; Male ; Middle Aged

Hemangioendothelioma, Epithelioid ; Humans ; Male ; Maxillary Sinus Neoplasms ; Middle Aged

Epithelioid hemangioendothelioma (HE) is a very rare malignant tumor that is pathologically benign tumor originating from endothelial cell but clinically presents metastasis and recurrence. A 29-year-old asymptomatic man, preoperatively diagnosed as lung cancer in the left lower lung, underwent a lobectomy, a wedge lung resection of left upper lung, and partial resection of diaphragm. Left lower lobar lesion was confirmed as pulmonary epithelioid hemangioendothelioma, but the lesions of the left upper lung and diaphragm were remained calcified by spontaneous regression of HE. We report a case of subcutaneous metastasis that occurred two times at 10 months and 19 months after previous surgical treatment of pulmonary EH.
Adult ; Diaphragm ; Endothelial Cells ; Hemangioendothelioma ; Hemangioendothelioma, Epithelioid* ; Humans ; Lung ; Lung Neoplasms ; Neoplasm Metastasis* ; Recurrence

Farber disease (FD) is a rare lysosomal storage disorder that shows autosomal recessive inheritance. We report the case of a 58-month-old girl with FD, who was misdiagnosed with epithelioid hemangioendothelioma. The patient had undergone five surgeries for sacrococcygeal masses and three surgeries for scalp masses owing to misdiagnosis. Here, we describe this rare case of FD.
Diagnostic Errors ; Farber Lipogranulomatosis* ; Female ; Hemangioendothelioma* ; Hemangioendothelioma, Epithelioid ; Humans ; Scalp ; Wills

Bone Neoplasms/diagnostic imaging* ; Hemangioendothelioma/surgery* ; Hemangioendothelioma, Epithelioid/surgery* ; Humans ; Precancerous Conditions