1.A Case of Kennedy Syndrome Mimicking Myasthenia Gravis.
Byung Ju LEE ; Ki Han KWON ; Sung Min KIM ; Ha Ry NA ; Byung Chul LEE ; Sang Hyo RYU ; Jae Chun BAE ; Jee In KIM ; Jin Sung LEE
Journal of the Korean Neurological Association 2001;19(5):544-546
Patients with Kennedy syndrome, which progresses more slowly than amyotrophic lateral sclerosis show a mild degree of motor fluctuation but rarely show significant decremental responses to repetitive nerve stimulations. Even in a patient with decremental responses to repetitive nerve stimulations, there is usually no significant improvements in motor symptoms to anticholinesterases. We experienced a patient with Kennedy syndrome, who showed significant decremental responses to repetitive nerve stimulations and a marked degree of motor fluctuation. His motor fluctuation responded dramatically to anticholinesterase. (J Korean Neurol Assoc 19(5):544~546, 2001)
Amyotrophic Lateral Sclerosis
;
Bulbo-Spinal Atrophy, X-Linked*
;
Cholinesterase Inhibitors
;
Humans
;
Myasthenia Gravis*
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