‘Scimitar’ syndrome in adulthood is usually asymptomatic.
Significant structural abnormalities symptoms usually
manifest early during infancy or young childhood with
features of congestive heart failure from significant shunting
of the anomalous pulmonary venous drainage. Diagnosis of
‘Scimitar’ Syndrome in adults is rare and usually an
incidental finding on chest radiograph. Here, we report a
case of an adult who presented with symptoms in her 40’s.
This syndrome has never been reported nor discussed in
Malaysia. This is the first case report of ‘Scimitar’ Syndrome
in Malaysian literature. The diagnostic dilemma, medical
management, and multi-disciplinary management by
cardiology, physiotherapy and pulmonary rehabilitation
teams are discussed.