No abstract available.
Facial Hemiatrophy* ; Lung*

Adult ; Facial Hemiatrophy ; Humans ; Male

Arm ; Facial Hemiatrophy ; Humans ; Skeleton

Disease Progression ; Facial Hemiatrophy ; surgery ; Humans

Romberg's disease manifests as progressive hemifacial atrophy of skin, soft tissue, and bone. Treatment involves three-dimensional reconstruction of all soft- tissue and skeletal disturbances. Soft-tissue reconstruction is directed at augmentation of deficient soft-tissue volume and there are many therapeutic modalities available, such as autologous tissue grafts and inorganic implants. The arrival of microsurgical techniques has improved the outlook for facial contour restoration. The tissues used for microsurgical tissue transfer include groin, scapular, and omentum. This article introduces our experience with the superior gluteal perforator-based flap for the restoration of facial contour defects in the patient of Romberg`s disease. Superior gluteal perforator flap has some advantages; It doesn`t need to transect or sacrifice of the gluteus maximus muscle, Flap elevation time is short, Blood flow of the perforator is reliable, There is no post-operative hindrance to walking in patient. The disadvantages of this perforator-based flaps are the anatomical variation in the location of perforators and the need for tedious dissection.
Facial Hemiatrophy ; Groin ; Humans ; Omentum ; Perforator Flap ; Skin ; Transplants ; Walking

Hemimasticatory spasm is a rare disorder that often accompanies facial hemiatrophy and is characterized by spasm in one or more of the jaw-closing muslces supplied by the fifth cranial nerve. We report a clinical and electrophysiological observation of a patient of hemimasticatory spasm, who presented involuntary spasm on masseter muscle and hemiatrophy of the face on the right side for 7 years.
Facial Hemiatrophy ; Humans ; Masseter Muscle ; Spasm* ; Trigeminal Nerve

Progressive facial hemiatrophy (PFH) was first described by Parry and Romberg and this is a rare disorder of an unknown origin. PFH is characterized by slowly progressive, mostly unilateral facial atrophy of the skin, soft tissues, muscles and underlying bony structures and is usually develops in the first or second decade of life. Although the clinical presentation of PFH may appear similar to localized linear scleroderma en coup the sabre, some patients presenting with PFH have neither en coup the sabre nor generalized sclerosis. Herein, we report on an unusual case of a 7-year-old girl who presented with progressive hemiatrophy of the face.
Atrophy ; Child ; Facial Hemiatrophy ; Humans ; Muscles ; Scleroderma, Localized ; Sclerosis ; Skin

facial augmentation was done by augmentation of the dermal-fat tissue. The progressive hemifacial atrophy is hard to treat by only one procedure and many modalites must be considered.]]>
Atrophy ; Collagen ; Facial Hemiatrophy ; Muscles ; Orthognathic Surgery ; Subcutaneous Fat ; Transplants

Diagnosis, Differential ; Facial Asymmetry ; congenital ; diagnosis ; surgery ; Facial Hemiatrophy ; diagnosis ; Humans ; Hypertrophy ; Orthodontics, Corrective

Parry and Romberg described progressive facial hemiatrophy, characterized by progressive unilateral wasting of the skin, fat, muscle and bone in 1825 and 1846, respectively. Involvement of the central nervous system, with impairment of neurologic function, occurs infrequently. Linear scleroderma on frontal and parietal scalp, named 'en coup de sabre', is considered an overlapping condition. An 11 year-old girl was presented to our office with left facial hemiatrophy and transverse linear band-like alopecia on her posterior parietal scalp. Histopathologically, there was a sclerotic change of the collagen fibers and dermal lymphocytic infiltrations around the skin appendages. Her skin lesion has improved by intralesional corticosteroid injection. Linear scleroderma frequently coexists with Parry-Romberg syndrome. But in this case, she had a unique pattern of scleroderma, which is distinct from the previously reported cases.
Alopecia ; Central Nervous System ; Collagen ; Facial Hemiatrophy ; Muscles ; Scalp ; Scleroderma, Localized ; Skin