No abstract available.
Facial Hemiatrophy* ; Lung*

Adult ; Facial Hemiatrophy ; Humans ; Male

Arm ; Facial Hemiatrophy ; Humans ; Skeleton

Disease Progression ; Facial Hemiatrophy ; surgery ; Humans

Romberg's disease manifests as progressive hemifacial atrophy of skin, soft tissue, and bone. Treatment involves three-dimensional reconstruction of all soft- tissue and skeletal disturbances. Soft-tissue reconstruction is directed at augmentation of deficient soft-tissue volume and there are many therapeutic modalities available, such as autologous tissue grafts and inorganic implants. The arrival of microsurgical techniques has improved the outlook for facial contour restoration. The tissues used for microsurgical tissue transfer include groin, scapular, and omentum. This article introduces our experience with the superior gluteal perforator-based flap for the restoration of facial contour defects in the patient of Romberg`s disease. Superior gluteal perforator flap has some advantages; It doesn`t need to transect or sacrifice of the gluteus maximus muscle, Flap elevation time is short, Blood flow of the perforator is reliable, There is no post-operative hindrance to walking in patient. The disadvantages of this perforator-based flaps are the anatomical variation in the location of perforators and the need for tedious dissection.
Facial Hemiatrophy ; Groin ; Humans ; Omentum ; Perforator Flap ; Skin ; Transplants ; Walking

Hemimasticatory spasm is a rare disorder that often accompanies facial hemiatrophy and is characterized by spasm in one or more of the jaw-closing muslces supplied by the fifth cranial nerve. We report a clinical and electrophysiological observation of a patient of hemimasticatory spasm, who presented involuntary spasm on masseter muscle and hemiatrophy of the face on the right side for 7 years.
Facial Hemiatrophy ; Humans ; Masseter Muscle ; Spasm* ; Trigeminal Nerve

Progressive facial hemiatrophy (PFH) was first described by Parry and Romberg and this is a rare disorder of an unknown origin. PFH is characterized by slowly progressive, mostly unilateral facial atrophy of the skin, soft tissues, muscles and underlying bony structures and is usually develops in the first or second decade of life. Although the clinical presentation of PFH may appear similar to localized linear scleroderma en coup the sabre, some patients presenting with PFH have neither en coup the sabre nor generalized sclerosis. Herein, we report on an unusual case of a 7-year-old girl who presented with progressive hemiatrophy of the face.
Atrophy ; Child ; Facial Hemiatrophy ; Humans ; Muscles ; Scleroderma, Localized ; Sclerosis ; Skin

facial augmentation was done by augmentation of the dermal-fat tissue. The progressive hemifacial atrophy is hard to treat by only one procedure and many modalites must be considered.]]>
Atrophy ; Collagen ; Facial Hemiatrophy ; Muscles ; Orthognathic Surgery ; Subcutaneous Fat ; Transplants

Diagnosis, Differential ; Facial Asymmetry ; congenital ; diagnosis ; surgery ; Facial Hemiatrophy ; diagnosis ; Humans ; Hypertrophy ; Orthodontics, Corrective

Progressive facial hemiatrophy, also known as Parry-Romberg syndrome, is a progressive and self-limited deformation of the subcutaneous tissue volume on one side of the face that creates craniofacial asymmetry. We present the case of a patient with a five-year history of progressive right facial hemiatrophy, who underwent facial volumetric restoration using cell-assisted lipotransfer (CAL), which consists of an autologous fat graft enriched with adipose-derived stem cells (ASCs) extracted from the same patient. ASCs have the capacity to differentiate into adipocytes. They also promote angiogenesis, release angiogenic growth factors, and some can survive as stem cells. The use of autologous fat as a filler in soft tissue atrophy has been satisfactory in patients with mild and moderate Parry-Romberg syndrome. Currently, CAL has showed promising results in the long term by decreasing the rate of fat reabsorption. The permanence and stability of the graft in all the injected areas has showed that autologous fat grafts enriched with stem cells could be a promising technique for the correction of defects caused by this syndrome.
Adipocytes ; Atrophy ; Facial Hemiatrophy ; Humans ; Intercellular Signaling Peptides and Proteins ; Stem Cells ; Subcutaneous Tissue ; Tissue Therapy ; Transplants