No abstract available.
Facial Hemiatrophy* ; Lung*

Adult ; Facial Hemiatrophy ; Humans ; Male

Arm ; Facial Hemiatrophy ; Humans ; Skeleton

Disease Progression ; Facial Hemiatrophy ; surgery ; Humans

Hemimasticatory spasm is a rare disorder that often accompanies facial hemiatrophy and is characterized by spasm in one or more of the jaw-closing muslces supplied by the fifth cranial nerve. We report a clinical and electrophysiological observation of a patient of hemimasticatory spasm, who presented involuntary spasm on masseter muscle and hemiatrophy of the face on the right side for 7 years.
Facial Hemiatrophy ; Humans ; Masseter Muscle ; Spasm* ; Trigeminal Nerve

Romberg's disease manifests as progressive hemifacial atrophy of skin, soft tissue, and bone. Treatment involves three-dimensional reconstruction of all soft- tissue and skeletal disturbances. Soft-tissue reconstruction is directed at augmentation of deficient soft-tissue volume and there are many therapeutic modalities available, such as autologous tissue grafts and inorganic implants. The arrival of microsurgical techniques has improved the outlook for facial contour restoration. The tissues used for microsurgical tissue transfer include groin, scapular, and omentum. This article introduces our experience with the superior gluteal perforator-based flap for the restoration of facial contour defects in the patient of Romberg`s disease. Superior gluteal perforator flap has some advantages; It doesn`t need to transect or sacrifice of the gluteus maximus muscle, Flap elevation time is short, Blood flow of the perforator is reliable, There is no post-operative hindrance to walking in patient. The disadvantages of this perforator-based flaps are the anatomical variation in the location of perforators and the need for tedious dissection.
Facial Hemiatrophy ; Groin ; Humans ; Omentum ; Perforator Flap ; Skin ; Transplants ; Walking

Progressive facial hemiatrophy (PFH) was first described by Parry and Romberg and this is a rare disorder of an unknown origin. PFH is characterized by slowly progressive, mostly unilateral facial atrophy of the skin, soft tissues, muscles and underlying bony structures and is usually develops in the first or second decade of life. Although the clinical presentation of PFH may appear similar to localized linear scleroderma en coup the sabre, some patients presenting with PFH have neither en coup the sabre nor generalized sclerosis. Herein, we report on an unusual case of a 7-year-old girl who presented with progressive hemiatrophy of the face.
Atrophy ; Child ; Facial Hemiatrophy ; Humans ; Muscles ; Scleroderma, Localized ; Sclerosis ; Skin

facial augmentation was done by augmentation of the dermal-fat tissue. The progressive hemifacial atrophy is hard to treat by only one procedure and many modalites must be considered.]]>
Atrophy ; Collagen ; Facial Hemiatrophy ; Muscles ; Orthognathic Surgery ; Subcutaneous Fat ; Transplants

Diagnosis, Differential ; Facial Asymmetry ; congenital ; diagnosis ; surgery ; Facial Hemiatrophy ; diagnosis ; Humans ; Hypertrophy ; Orthodontics, Corrective

PURPOSE: Romberg's disease manifests as progressive hemifacial atrophy of the skin, soft tissue and bone, which usually begins in the first or second decade of life. When present, atrophy may originate from the cutaneous stigmata and may become so sharply delimited by the midline. METHODS: A 10-year-old girl, who had suffered from right mandibular area atrophy for 3 years, visited us and was diagnosed with Romberg's disease. The depressed lesion of the face was augmented successfully using a deepithelialized groin free flap. The superficial circumflex iliac vessels were used as the donor pedicle and the facial artery and vein were used as the recipient vessels. RESULTS: After surgery, the flap survived well and she was satisfied with the result. Although there are various methods of facial augmentation using free flaps, this flap has some advantages. First, there is a considerable amount of fat tissue components for augmentation. Second, flap elevation with thinning is possible. Third, the donor site can be hidden. CONCLUSION: The groin dermo-fat free flap is a good method for the facial augmentation of Romberg's disease.
Arteries ; Atrophy ; Child ; Christianity ; Facial Hemiatrophy ; Free Tissue Flaps ; Groin ; Humans ; Skin ; Tissue Donors ; Veins