A case of 17 years old male with KPP of Tbost-Unna Type is reported. The akin lesions were characterized by the presence of confluent, sharply demarcated hyperk eratotic plaques on the palmar and plantar surfaces. Hypercontraction of palms and soles and hyperhidro is of scalp, face, palms and soles were also noted. Roentogenologic study revealed secondary changes of osteoporosis, flexion deformity and osteoarthritis due to soft tissue contracture and phalangeal and metatarsal bones of hands and feet showed bony resorption with tapering appearance. Histalogic findings of palmar lesion showed excessive hyperkeratosis, parakeratosis and acantosis in the epidermis and no pathology was noted in the dermis and skin appendages, He was treated with hot water compress, 5% Salicylic acid ointment and vit. A and D for 2 months and favorable effect was noted. Authors reviewed relevant literature and made discussions also.
Adolescent ; Betazole ; Congenital Abnormalities ; Contracture ; Dermis ; Epidermis ; Foot ; Hand ; Humans ; Keratoderma, Palmoplantar* ; Keratosis* ; Male ; Metatarsal Bones ; Osteoarthritis ; Osteoporosis ; Parakeratosis ; Pathology ; Salicylic Acid ; Scalp ; Skin ; Water

No abstract available.
Takayasu Arteritis*

No abstract available.
Rhabdomyosarcoma*

PURPOSE: Knowing the optimal length of central venous catheterization is important in order to prevent complications provoked by inappropriate placement of the tip of central venous catheter. We evaluated the optimal lengths of central venous catheterization using 3-Dimensional Multi- Detector Row Computed Tomography (MDCT). METHODS: Between May 2005 and September 2005, we prospectively enrolled 122 consecutive patients who underwent elective chest MDCT. We reconstructed 3-dimensional MDCT images of the right internal jugular vein, right subclavian vein, left internal jugular vein, left subclavian vein and the superior vena cava/right atrium (SVC/RA) junction. In 3-dimensional images, we measured the distance from the puncture site of catheterization to the SVC/RA junction. In addition, we analyzed the correlation of the length of central vein to demographic findings, including patients' height, weight, body mass index, and body surface area (BSA). By regression modeling, we derived formulas to calculate the optimal lengths for central venous catheterization. RESULTS: The optimal lengths of central venous catheterization via the right internal jugular vein, right subclavian vein, left internal jugular vein, and left subclavian vein were 12.9+/-1.5 cm, 14.0+/-1.5 cm, 15.9+/-1.9 cm, and 17.9+/-1.4 cm, respectively. The optimal length of right subclavian catheterization correlated significantly with body weight and BSA (p<0.01). The optimal length of left internal jugular approach correlated well with height (p<0.01), body weight, BMI, and BSA (p<0.005). CONCLUSION: The optimal lengths of central venous catheter were measured by 3-dimensional MDCT and correlated with demographic findings. By regression modeling, we developed formulas to predict the optimal length of central venous catheterization using based on demographic findings.
Body Surface Area ; Body Weight ; Catheterization ; Catheterization, Central Venous* ; Catheters ; Central Venous Catheters* ; Humans ; Jugular Veins ; Prospective Studies ; Punctures ; Subclavian Vein ; Thorax ; Veins

No abstract available.
Neuroblastoma*

Intra-abdominal pregnancy is uncommon occurrence, constituting only 1% of all ectopic pregnancy. It is usually the result of a tubal or ovarian pregnancy that has aborted or ruptured into the peritoneal cavity. However, the complications of abdominal pregnancy can be devastating. Premature placental separation with massive hemorrhage, hypofibrinogenemia following fetal demise, and suppuration and abscess formation lead to producing maternal health risk. A perinatal mortality and maternal mortality were 85-95% and 0.5-6% respect-ively, from the world literature. Optimal obstetrical care requires early diagnosis and prompt surgical intervention. Recently, a patient presented to the St.Francisco general Hospital with a retained abdominal pregnancy of 6 years duration without complications, as discussed below.
Abscess ; Early Diagnosis ; Female ; Hemorrhage ; Hospitals, General ; Humans ; Maternal Mortality ; Maternal Health ; Perinatal Mortality ; Peritoneal Cavity ; Pregnancy ; Pregnancy, Abdominal* ; Pregnancy, Ectopic ; Suppuration

No abstract available.
Flushing* ; Liver Transplantation* ; Liver*

Purpose: The aim of this study was to compare surgical outcomes after liver resection for hepatocellular carcinoma (HCC) according to tumor size using a large, nationwide cancer registry-based cohort and propensity score matching. Methods: From 2008 to 2015, a total of 12,139 patients were diagnosed with liver cancer and registered in the Korean Primary Liver Cancer Registry. Patients without distant metastasis who underwent hepatectomy as a primary treatment were selected. We performed 1:1 propensity score matching between the small (<5 cm), large (≥5 cm and <10 cm), and huge (≥10 cm) groups. Results: Overall, 265 patients in the small and large groups were compared, and 64 patients each in the large and huge groups were compared. The overall and progression-free survival rates were significantly lower in the large group than in the small group (P < 0.001 and P < 0.001, respectively). Overall survival tended to be poorer in the huge group than in the large group (P = 0.051). The progression-free survival rate was significantly lower in the huge group than in the large group (P = 0.002). Conclusion Although primary liver resection can be considered even in patients with huge HCC, greater caution with careful screening for recurrence is needed.

No abstract available.
Pulmonary Atresia*

PURPOSE: Alcohol consumption is an important risk factor for injury. It is controversial, however, whether alcohol also has an effect on the severity of injury. We tried to evaluate the effect of alcohol on the severity of injury, especially on the severity of blunt injury due to traffic accidents, falls, collisions, and so on. METHODS: We used the ED-based injury registry in a regional emergency center. During two months, 831 victims were registered. We enrolled 397 patients who were over 15 years and had been injured by blunt trauma. We classified them into two groups by alcohol consumption. Positive alcohol consumption was defined as that positively confirmed by the victims or guardians, or that suspected on physical examination. The injury severity was measured by using the New Injury Severity Score, the Revised Trauma Score, the Trauma and Injury Severity Score (TRISS), the probability of survival of TRISS, and the International Classification of Disease 10th-version-based Injury Severity Score. RESULTS: Alcohol consumption was significantly larger in males than in females, in intentional injuries than in accidental injuries, in injury mechanisms other than traffic accident injuries, and in nighttime injuries than daytime injuries. However, the injury severity for the two groups was not significantly different. In the subgroup analysis, alcohol did not seem to affect the severity of injury due to any of the individual injury mechanisms. CONCLUSION: Alcohol consumption has no significant effect on the severity of blunt injuries.
Accidents, Traffic ; Alcohol Drinking* ; Classification ; Emergencies ; Female ; Humans ; Injury Severity Score ; Male ; Physical Examination ; Risk Factors ; Wounds and Injuries ; Wounds, Nonpenetrating*