No abstract available.
Erythromelalgia* ; Thorax*

No abstract available.
Arterial Pressure* ; Aspirin ; Erythromelalgia* ; Thrombocytosis

Skin biopsy with investigation of small nerve fiber in human epidermis and dermis has been proven to be a useful method for demonstration of small fiber neuropathy. Quantification of intraepidermal nerve fiber density using anti-Protein Gene Product 9.5 (PGP 9.5) antibody is standardized method to diagnose the small fiber neuropathy. Skin biopsy method also makes it possible to differentiate the type of nerve fibers by using different antibodies. Quantification of dermal structures with different type of nerve fibers could be used to invest pathophysiologic mechanism of diseased state.
Antibodies ; Biopsy* ; Dermis ; Epidermis ; Erythromelalgia ; Humans ; Nerve Fibers* ; Skin*

Acupuncture Points ; Acupuncture Therapy ; Adolescent ; Erythromelalgia ; therapy ; Female ; Humans

Erythromelalgia ; complications ; Female ; Humans ; Mercury Poisoning ; complications ; Middle Aged

Erythromelalgia (EM) is an uncommon disorder characterized by redness, heat, and painful extremities with intense burning sensation. Attacks of EM may be worsened by limb warming, exercise, or dependency of the affected extremity. Although the coexistence of EM and Raynaud's phenomenon (RP) may appear to be opposites in symptomatology and clinical presentation, recent studies provide an explanation based on a dysfunction of the regulation of vasomotor tone. Here, we report a case of EM in a patient with RP.
Burns ; Erythromelalgia ; Extremities ; Hot Temperature ; Humans ; Lupus Erythematosus, Systemic ; Sensation

Erythromelalgia(EM) is a rare clinical syndrome characterized by the triad of redness, increased temperature, and pain of the extremities. The patient was a 69-year-old woman presented erythematous tender patches on both palms and soles. Laboratory and clinical investigations revealed an underlying myeloproliferative disorder. Histologic examination of the erythema on her foot showed some vessels with thickened endothelial walls and partially obstructed lumens by organized thrombi. Hydroxyurea used for the treatment of polycythemia vera eliminated the skin lesions and symptoms of erythromelalgia. We report a case of secondary erythromelalgia associated with polycythemia vera.
Aged ; Erythema ; Erythromelalgia* ; Extremities ; Female ; Foot ; Humans ; Hydroxyurea ; Myeloproliferative Disorders ; Polycythemia Vera* ; Polycythemia* ; Skin

Primary erythromelalgia is a rare condition that's characterized by erythema, an increased skin temperature and burning pain in the extremities. The pain is often very severe, and treating erythromelalgia is frustrating and difficult. We report here on the case of a 12-year old girl with primary erythromelalgia in both lower extremities. The pain was refractory to medical treatment, but a bilateral sympathetic block with lidocaine and triamcinolone resulted in relief from the pain. Our experience with this disease demonstrates that sympathetic blocks are effective in improving the symptoms and they may be attempted on erythromelalgia patients who do not respond to other treatments, including medication and epidural blocks.
Burns ; Erythema ; Erythromelalgia ; Extremities ; Humans ; Lidocaine ; Lower Extremity ; Skin Temperature ; Triamcinolone

An 18-year-old man had suffered from intense burning with redness and an increased temperature of both the lower legs, forearms and hands since the age of 5. Symptoms were exacerbated by exposure to heat or walking. The patient obtained temporary relief by immersing his feet and hands in cold water. We observed the increase of skin temperature in relation to pain by thermography. No specific abnormalities were noted in laboratory studies. Treatment with aspirin was ineffective. We report a rare case of primary erythermalgia with typical features.
Adolescent ; Aspirin ; Burns ; Erythromelalgia* ; Foot ; Forearm ; Hand ; Hot Temperature ; Humans ; Leg ; Skin Temperature ; Thermography ; Walking ; Water

An 8-year-old female has suffered from intense burning with redness and increased temperature of the feet and hands since 5-year-old. We observed increase of the skin temperature in relation of pain attack by the digital thermometer and the color television thermography. No specific abnormalities were noted in the laboratory studies. Treatment with various systemic and topical medication revealed of unfavorable result, but for the conservative mangement, the pain was relieved by the exposure to the cold environment-laying bare in the outdoors and the wind of the electric fan.
Burns ; Child ; Child, Preschool ; Erythromelalgia* ; Female ; Foot ; Hand ; Humans ; Skin Temperature ; Television ; Thermography ; Thermometers ; Wind