The association of varicose vein, soft tissue and bony hypertrophy and. cutaneous hemangioma of the "port-wine" variety confined to one extremity was first reported in l900 by Klippel and Trenaunay, and then Weber. Their reports are generally considered today represent variations of the same syndrome. The vascular abnormalities may be any type of hemangioma, arteriovenous fistula, or lymphangioma appearing at birth or in infancy. The trophic changes almost always involve only one limb. The authors reported a case of Klippel-Trenaunay-Weber(K-T-W) syndrome in seven- year-old boy consisted of nevus flammeus associated with hypertrophy, elongation and heating sensation except varicose or arteriovenous fistula of the left leg.
Arteriovenous Fistula ; Brain Stem Infarctions* ; Extremities ; Heating ; Hemangioma ; Hot Temperature ; Humans ; Hypertrophy ; Leg ; Lymphangioma ; Male ; Parturition ; Port-Wine Stain ; Sensation ; Varicose Veins