1.Adult Onset Still’s Disease: A Case Report in Hospital Kuala Lumpur
Choon Sian Lee ; Li Lian Tay ; Gin Peng Chan ; Zuliatul Faizah Baharom ; Bang Rom Lee ; Suganthi Thevarajah ; Min Moon Tang
Malaysian Journal of Dermatology 2020;44(1):41-49
Adult onset Still’s disease (AOSD) is a sporadic
complex autoinflammatory syndrome first described
in 1971.1 It is characterised by high spiking fever,
polyarthritis, sore throat, lymphadenopathy,
hepatosplenomegaly, serositis, and evanescent skin
eruptions.1,2 It is associated with life-threatening
complications too. Diagnosis of AOSD is laborious
as it requires extensive investigations to exclude
infections, autoimmune diseases and malignancy.
Here we illustrate a young female who exhibited a
turbulent presentation of ASOD.