1.Myxoid Chondrosarcoma of the Sinonasal Cavity in a Child: a Case Report.
Yeo Ju KIM ; Soo Ah IM ; Gye Yeon LIM ; Ho Jong CHUN ; Hyun Jin PARK ; Min Sik KIM ; Yeong Jin CHOI
Korean Journal of Radiology 2007;8(5):452-455
Chondrosarcomas are malignant tumors of cartilage that rarely involve the sinonasal region, and myxoid chondrosarcoma is a rare histologic variant of chondrosarcoma that usually occurs in the soft tissue of extremities. Although several case reports and results of small series of chondrosarcomas in the sinonasal region in children are available, myxoid type chondrosarcoma is extremely rare. We recently experienced a case of low grade myxoid chondrosarcoma involving the sinonasal cavity in a 10-year-old boy, and here we report its radiologic-pathologic findings. In this case, chondroid calcification on CT and septal and marginal enhancement on MRI suggested a chondrosarcoma. Whole body PET-CT demonstrated no definite metastatic lesion and a low peak standardized uptake value primary tumor. However, no definite distinguishing imaging features were observed that distinguished low grade myxoid chondrosarcoma from conventional chondrosarcoma.
Bone Neoplasms/*diagnosis/radiotherapy/surgery
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Child
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Chondrosarcoma/*diagnosis/radiotherapy/surgery
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Diagnosis, Differential
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Follow-Up Studies
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Humans
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Magnetic Resonance Imaging
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Male
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Myxosarcoma/*diagnosis/radiotherapy/surgery
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Nasal Cavity/*pathology/*radiography/surgery
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Paranasal Sinuses/*pathology/*radiography/surgery
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Positron-Emission Tomography
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Rare Diseases
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Tomography, X-Ray Computed
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Whole Body Imaging
2.Naso-oropharyneal chordoma: a clinicopathological analysis of 12 cases.
Lan LIN ; Shu-yi WANG ; Jian WANG
Chinese Journal of Pathology 2009;38(3):194-195
Adenocarcinoma, Mucinous
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pathology
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Adult
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Aged
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Chondrosarcoma
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pathology
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Chordoma
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pathology
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radiotherapy
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surgery
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Combined Modality Therapy
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Diagnosis, Differential
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Female
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Follow-Up Studies
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Humans
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Male
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Middle Aged
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Nasopharyngeal Neoplasms
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pathology
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radiotherapy
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surgery
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Neoplasm Recurrence, Local
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Paranasal Sinus Neoplasms
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pathology
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radiotherapy
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surgery
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Retrospective Studies
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Sphenoid Sinus
3.Meningeal hemangiopericytoma: a clinicopathologic study of 17 cases.
Hai-Bo WU ; Hai-Yan WENG ; Min DING ; Ping GU ; Xiao-Qiu WANG ; Wen ZHONG
Chinese Journal of Pathology 2011;40(4):251-252
Adult
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Aged
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Antigens, CD34
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metabolism
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Chondrosarcoma, Mesenchymal
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metabolism
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pathology
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Diagnosis, Differential
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Female
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Follow-Up Studies
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Hemangiopericytoma
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metabolism
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pathology
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radiotherapy
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surgery
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Humans
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Male
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Meningeal Neoplasms
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metabolism
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pathology
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radiotherapy
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surgery
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Meningioma
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metabolism
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pathology
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Middle Aged
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Neoplasm Recurrence, Local
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Proto-Oncogene Proteins c-bcl-2
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metabolism
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Solitary Fibrous Tumors
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metabolism
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pathology
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Vimentin
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metabolism
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Young Adult