No abstract available.
Cholangitis, Sclerosing*

No abstract available.
Cholangitis, Sclerosing* ; Diagnosis* ; Immunoglobulins*

Cholangitis, Sclerosing ; diagnosis ; therapy ; Humans

No abstract available.
Cholangitis, Sclerosing ; Critical Illness ; Humans

Immunoglobulin G4-related disease (IgG4-RD) is a systemic fibroinflammatory condition of which IgG4-related sclerosing cholangitis (IgG4-SC) is the biliary manifestation. In this review, we provide an overview of IgG4-RD, with a focus on the biliary manifestations. In particular, we describe the important differential diagnoses of IgG4-SC, namely, primary sclerosing cholangitis and cholangiocarcinoma, outline diagnostic criteria for IgG4-SC, provide insight into possible pathophysiological mechanisms underlying the disease and discuss short and long-term management options of this recently described disease.
Cholangiocarcinoma ; Cholangitis, Sclerosing* ; Diagnosis, Differential ; Immunoglobulins*

Autoimmune pancreatitis or IgG4-related sclerosing cholangitis often involves the liver. Most common lesion involving the liver is shown as mass or masses often referred as inflammatory pseudotumor. Inflammatory pseudotumor usually needs to be discriminated with malignancy. Here we report a case of IgG4-related sclerosing cholangitis with liver involvement presented as a mass. It was proven by biopsy and did not show any evidence of autoimmune pancreatitis. The mass infiltrated around the portal tract and portal vein thrombosis was also present.
Biopsy ; Cholangitis, Sclerosing* ; Granuloma, Plasma Cell ; Liver* ; Pancreatitis ; Venous Thrombosis

Primary sclerosing cholangitis (PSC) is a rare disease entity. The medical therapy for PSC has not been reasonably beneficial. Thus liver transplantation is known to be the ultimate therapy. Because liver transplantation for PSC has been performed rarely in Korea, we report a case of liver transplantation for PSC with a review of the literature. A 35-year-old male was admitted to our hospital with recurrent jaundice for seven years. ERCP showed multiple strictures of intrahepatic duct and an irregularity of the extrahepatic duct wall. Despite medication and endoscopic treatment, liver functions did not imporve and clinical status got worsened. Thus liver transplantation was performed for the correction of hepatic failure. Two months after transplantation, liver functions and general weakness gradually improved and now, one year after liver transplantation, the patient is in normal life.
Adult ; Cholangitis, Sclerosing/diagnosis/*surgery ; Humans ; *Liver Transplantation ; Male

The technique of intraductal ultrasonography (IDUS) of the bile duct with a thin-caliber probe and a ropeway system has provided excellent images of the bile duct and periductal structures and is an easy transpapillary approach. In addition, once the guide wire is inserted into the bile duct, IDUS and transpapillary biopsy after endoscopic retrograde cholangiopancreatography can be performed in a single session. Here, we review the usefulness of IDUS in the diagnosis of cholangiocarcinoma and IgG4-related sclerosing cholangitis.
Bile Ducts ; Biopsy ; Cholangiocarcinoma ; Cholangiopancreatography, Endoscopic Retrograde ; Cholangitis, Sclerosing

Cholangitis, Sclerosing ; complications ; Histiocytosis, Langerhans-Cell ; etiology ; Humans

Primary sclerosing cholangitis, a chronic cholestatic liver disease, is uncommon and is characterized byinflammation and fibrosis of the bile ducts. It frequently occurs in association with ulcerative colitis. Wedescribe two cases of primary sclerosing cholangitis in patients with ulcerative colitis.
Bile Ducts ; Cholangitis ; Cholangitis, Sclerosing* ; Colitis, Ulcerative* ; Fibrosis ; Humans ; Liver Diseases ; Ulcer*