Acromelanosis progressiva is a peculiar progressive pigmentary disorder characterized by intensely dark and sharply demarcated hyperpigmentation over the dorsa of fingers and toes, and the pigmentation rapidly spread proximally. A 19-year-old female had sharply demarcated symmetric dark aroarn macules on the dorsa of her hands and feet, forearms, lower legs, face and neck. These pigmentations at first appeared at the age of 5 on the dorsa of her fingers and toes, thereafter these pigmertatons spread progressively to the proximal portion of her body. Histologically, a proliferation of mela biocyte at the epidermal-dermal junction was seen, associated with mild hyperkeratosis. She was othervise normal on physical examination and had no family historv of consanguinity.
Consanguinity ; Female ; Fingers ; Foot ; Forearm ; Hand ; Humans ; Hyperpigmentation ; Leg ; Neck ; Physical Examination ; Pigmentation ; Toes ; Young Adult

The authors report a case of cirsoid aneurysm in which diagnosis is reached by carotid angiography. To clarify the confusion regarding this rare lesion, the definition, origin and pathogenesis of the lesion are discussed.
Aneurysm* ; Angiography ; Diagnosis ; Scalp*

BACKGROUND AND OBJECTIVES: Pseudo-labyrinthine symptom without any other accompanying neurologic symptoms or signs occur with cerebellar infarction. The prognosis and management of cerebellar infarction differ from those of vertigo associated with unilateral vestibulopathy. The objective of study was to analyze the clinical symptoms of cerebellar infarction mimicking unilateral vestibulopathy according to the infarction territory. MATERIALS AND METHOD: Among 273 patients who showed pseudo-labyrinthine symptoms or signs, 28 patients were diagnosed cerebellar infarction on MRI between January 2003 and October 2006. Out of the 28 patients, 9 patients accompanying with focal neurologic symptoms or signs in early stage were excluded, and a retrospective analysis of total 19 patients was done through chart reviews. Using diffusion-weighted imaging, we divided 19 patients into two groups, AICA and PICA territory infarction. Clinincal features, outcome of audiologic and vestibular function test were compared between the groups. RESULTS: Among the 19 subjects, 10 were males and 9 were females, the mean age was 63.1+/-.0. On MRI, 5 (26.3%) subjects showed infarction in unilateral AICA territory, 14(73.7%) in unilateral PICA territory. In the patients with AICA territory infarction, audiological tests confirmed unilateral sensorineuronal hearing loss in all 5 subjects. On V-ENG, 4/5 (80%) demonstrated horizontal or mixed horizontal torsional spontaneous nystagmus, and 4/5 (80%) had a canal paresis to caloric stimulation. In several days of hospital stay, 3/5 (60%) showed new neurologic signs, facial numbness. In the patients with PICA infarction, there was no hearing change. On V-ENG, 12/14(85.7%) demonstrated horizontal or mixed horizontal torsional spontaneous nystagmus, and 7/14 (50%) had a canal paresis to caloric stimulation. In several days of hospital stay, 10/14 (71.4%) accompanied with cerebellar ataxia. CONCLUSION: Cerebellar infarction simulating unilateral vestibulopathy is more common than previously thought. Early recognition of the cerebellar infarction showing pseudo-vestibular symptom may allow specific management. Also taking into account that clinical features differ by infarction territory will assist in determining the patient's status of the disease.
Cerebellar Ataxia ; Cerebellum ; Female ; Hearing ; Hearing Loss ; Humans ; Hypesthesia ; Infarction* ; Length of Stay ; Magnetic Resonance Imaging ; Male ; Neurologic Manifestations ; Paresis ; Pica ; Prognosis ; Retrospective Studies ; Vertigo ; Vestibular Function Tests

Intraarterial digital subtraction angiography(IADSA) was developed to subjugate the disadvantages of intravenous digital subtraction angiography(IVDSA). Recently, its utility has been increased in renal diseases. For investigation of clinical significance of IADSA in renal diseases, we analysed with 22 patients that renal IADSA had been performed in during the period from May, l984 to January, l986. The following results were obtained; l. Indications of the renal IADSA were renal bleeding, flank mass, hypertension and abnormality IVP or RGP only. 2. Diagnostic accuracy of the renal IADSA in renal diseases was 82.4%. 3. Renal toxicity and pain could be reduced due to decreased dose and dilution of contrast material. 4. Utilization of embolotherapy was increased because of better imaging of the renal vascularity and shortened examination-time of renal IADSA. 5. Renal IADSA can be substituted for conventional renal angiography and renal IVDSA in almost all renal diseases.
Angiography ; Angiography, Digital Subtraction* ; Embolization, Therapeutic ; Hemorrhage ; Humans ; Hypertension

Liposarcoma is the malignant tumor that can be originated from any adipose tissue. Spermatic cord liposarcoma are very rare. They are less than 4% of primary malignant tumor of spermatic cord. Radical orchiectomy appears to be adequate treatment. We report a case of liposarcoma of the left spermatic cord in 54 years old man which has presented as a slowly growing scrotal mass without metastatic evidence and radical orchiectomy were performed as a treatment. The iteratures were reviewed briefly.
Adipose Tissue ; Humans ; Liposarcoma* ; Middle Aged ; Orchiectomy ; Spermatic Cord*

The authors report a rare case of reticulum cell sarcoma-microgliomatosis which was extended into the leptomeninges, the Virchow-Robin spaces and choroid plexus invading the cerebral parenchyma in the left temporal area. Histogenesis of this tumor is briefly discussed.
Brain* ; Choroid Plexus ; Lymphoma, Non-Hodgkin* ; Reticulum*

The authors describe a case of ossiculum terminale in which a new technique of posterior cervical fusion for the reduction of atlantoaxial dislocation has been attempted, and satisfactory stabilization and restoration of normal contour of the cervical spine have been obtained by double wiring technique.
Dislocations* ; Spine

The authors analyze arbitrary 100 cases of skull fractures and compare with the incidence and character of the complication of head injuries associated with a skull fracture. Age, sex, cause of injury, skull fracture, intracranial hemorrhage, mortality rate and sequelae are discussed.
Craniocerebral Trauma ; Incidence ; Intracranial Hemorrhages ; Mortality ; Skull Fractures* ; Skull*

Although a great deal has been written about porencephaly during the past 100 years, there is much that remains obscure. The clinical recognition of porencephaly is important because it occurs with sufficient frequency to require consideration in the differential diagnosis of focal cerebral lesions. The authors considered and discussed to fulfill the pathogensis for this case.
Diagnosis, Differential

Congenital anterior urethral diverticulum is presented as a cause of urinary tract obstruction and is rate in young male. We report a case of congenital anterior urethral diverticulum developed in 3 year old male child.
Child ; Child, Preschool ; Diverticulum* ; Humans ; Male ; Urinary Tract