Choriostomas represent the most common epibulbar lesions in the pediatric age group. Generally, they are on the surface and do not involve the deeper layer of cornea or sclera. Epibulbar dermoids frequently cause amblyopia and cosmetic problems due to high astigmatism and the presence of the tumor. Surgery is the only option for epibulbar dermoids. Lamellar or penetrating keratoplasty has been advocated depending on the site and the depth of the epibulbar dermoids. However, the outcome is not always promising due to accompanying amblyopia and high incidence of vascularization of the grafts. In the present article we report a case of epibulbar choriostomas in the right eye of a 5-year-old, non-syndromic girl who underwent right limbal dermoid excision with lamellar keratoplasty.Postoperatively she was improved cosmetically, however the astigmatism and the vision remained the same. Therefore the amblyopic therapy should be emphasized postoperatively.