Dystrophic epidermolysis bullosa is a rare, chronic non-inflammatory bullous disease, which easily forms bullae by minor mechanical trauma or spontaneously, is inherited either in an autosomal dominant or autosomal recessive fashion. We report herein two cases which presented with bullae, erosions and ulcers on extremities, buttock, chest, abdomen and face and loss of all nail since birth in two sisters. Bulla occured bencath the basal lamina histopathologically, anchoring fibrils were almost absent on electron miaoscopy in both cases. The two sisters represented dystrophic epidermolysis bullosa considering the absence of family history inheritcd in an autosomal dominant fashion and the clinical, histological and electronmicroscopic findings.
Abdomen ; Basement Membrane ; Buttocks ; Epidermolysis Bullosa Dystrophica* ; Extremities ; Humans ; Parturition ; Siblings* ; Thorax ; Ulcer

No abstract available.

Localized fibrous tumor is an uncommon submesothelial origin tumor found in pleura most commonly. Sixty five-year-old man with right lower quadrant pain was admitted. He was treated with resection of tumor and was diagnosed as localized fibrous tumor of pelvic cavity. He is now being followed up without any evidence of recurrence for 34 months. This case is presented with reviewing references.
Pleura ; Recurrence

Cutaneous metastasis from renal cell carcinoma is not unusual, occurring in 3 to 7%, although it may be overlooked. We report a case of metastatic renal cell carcinoma in a 74-year-old man who was presented with a 1.5 x 1.5 x 0.5 cm-sized nodule on the right zygoma for 3 months. A skin biopsy demonstrated the typical clear cell adenocarcinoma with PAS(+) granules in the cytoplasm and honeycombed or glandular configuration, compatible with metastatic renal cell carcinoma. Kidney ultrasonogram and abdomina1 CT scanning showed a large cystic mass on the upper pole of the left kidney. Furthermore radiologic studies revealed multiple metastatic lesions in the lung, liver and brain. He died 4 months later.
Adenocarcinoma, Clear Cell ; Aged ; Biopsy ; Brain ; Carcinoma, Renal Cell* ; Cytoplasm ; Humans ; Kidney ; Liver ; Lung ; Neoplasm Metastasis ; Skin ; Tomography, X-Ray Computed ; Ultrasonography ; Zygoma*

Complications of penile prosthesis include malfunction, infection and patient dissatisfaction. Herein, a rare complication of a retained reservoir having eroded into the bladder after the removal of the penile components of a three-piece penile prosthesis, is reported. A 39-year-old man complained of irritative voiding symptoms. The symptoms had developed 4 years after the removal of the penile components of the prosthesis. The erosion of the reservoir into the bladder was discovered incidentally during the treatment of bladder calculi. The reservoir was removed by an open vesicolithotomy.
Adult ; Calculi ; Cytochrome P-450 CYP1A1 ; Humans ; Penile Prosthesis* ; Prostheses and Implants ; Urinary Bladder Calculi* ; Urinary Bladder*

No abstract available.
Fistula*

BACKGROUND: Post-intubation injury is known to be the most common cause of tracheal stenosis. Treatment strategy for tracheal stenosis varies accoring to the extent of pathologic lesion. Focal mucosal lesion can be treated with laser photoablation, but full thickness tracheal lesion should be treated with resection and anastomosis. MATERIAL AND METHOD: From Aptil 1998 to May 1999, twelve patients suffering from tracheal stenosis as a complication of endotracheal intubation were managed by resection and end-to-end anastomosis in the Department of Thoracic and Cardiovascular Surgery, Gyeongsang National University Hospital. RESULT: There was no operative mortality. Five temporary vocal cord paralysis and one wound infection occurred as early complications. During 18 months of follow-up, re-stenosis was not found. CONCLUSION: Tracheal resection and anastomosis can be considered as an excellent surgical treatment for tracheal stenosis which developed as a complication of endotracheal intubation.
Follow-Up Studies ; Humans ; Intubation, Intratracheal ; Mortality ; Tracheal Stenosis* ; Vocal Cord Paralysis ; Wound Infection

No abstract available.
Antibodies* ; Female ; Hepatitis B* ; Hepatitis* ; Humans ; Pregnant Women*

No abstract available.

Dissecting aneurysm involves development of a hematoma in the media of aorta, which is usually contagious with the lumen of the aorta via a tear in the media. The high percentage of co-existing diseases such as other cardiovascular diseases in these patients accounts for much of the surgical morbidity and mortality. Complications in Dacron patch graft surgery for repair of descending thoracic aortic aneurysm include massive hemorrhage, myocardial ischemia, myocardial infarction, heart failure, paraplegia and renal failure. A 60 year-old, 59kg woman underwent Dacron patch graft surgery for descending thoracic aortic aneurysm, under the high thoracic epidural block supplemented with light general anesthesia(N2O-O2). During operation, systolic blood pressure of upper extremities ranging from 120 mmHg to 100 mmHg was maintained, while diastolic pressure was maintained from 60 mmHg to 4) mmHg. Mean arterial pressure of 15-20 mmHg was maintained in lower extremities. When aorta was declamped, hypotension and bradycardia continued for 10 minutes. After administration of epinephrine and CaCl2, vital signs were stable. Total aorta cross-clamping time was 47 minutes, and total urine output was 200 ml. Although mannitol and steroid were administered for prevention, paraplegia occured postoperatively because of prolonged aorta cross clamping time.
Aneurysm, Dissecting ; Aorta ; Aortic Aneurysm, Thoracic* ; Arterial Pressure ; Blood Pressure ; Bradycardia ; Cardiovascular Diseases ; Constriction ; Epinephrine ; Female ; Heart Failure ; Hematoma ; Hemorrhage ; Humans ; Hypotension ; Lower Extremity ; Mannitol ; Middle Aged ; Mortality ; Myocardial Infarction ; Myocardial Ischemia ; Paraplegia* ; Polyethylene Terephthalates ; Renal Insufficiency ; Transplants ; Upper Extremity ; Vital Signs