Plexiform schwannoma is a rare benign tumor arising from the peripheral nerve sheath and characterized by a multinodular and plexiform growth pattern. This tumor usually arises sporadically. In rare cases, plexiform schwannomas have been associated with neurofibromatosis type 2. Plexiform schwannoma should be differentiated from plexiform neurofibroma, because the latter is pathognomonic tumor of neurofibromatosis type 1 and has a potential of malignant transformation. We report a case of multiple plexiform schwannomas associated with bilateral acoustic neuromas and meningioma.
Meningioma ; Neurilemmoma* ; Neurofibroma, Plexiform ; Neurofibromatoses* ; Neurofibromatosis 1 ; Neurofibromatosis 2* ; Neuroma, Acoustic ; Peripheral Nerves

Neurilemoma is a pure proliferation of Schwann cell and its ocular symptoms depend on the location of the tumor and its size. Neurofibromatosis is a multisystemic disease and has two distinct form : Neurofibromatosis type 1 described as peripheral neurofibromatosis and type 2 as central or bilateral acoustic neurofibromatosis. We experienced a case of orbital neurilemoma associated with neurofibromatosis in a 12-year-old male patient who presented with left orbital mass. We report this case with literature review.
Child ; Humans ; Male ; Neurilemmoma* ; Neurofibroma* ; Neurofibromatoses ; Neurofibromatosis 1 ; Neurofibromatosis 2 ; Orbit*

We performed a retrospective review on 32 patients(37 eyes) with the diagnosis of optic neuritis with follow-up more than 3 months, to determine its clinical characteristics in Korea. They consisted of 18 women and 14 men with a median age of 35.9 years. The initial visual acuity on presentation was variable from 1.2 to NLP, 84% of patients had at least 0.5 or better final visual acuity. Sixty-nine percent of the patients showed swollen disc and the remaining appeared normal in the affected eyes. Visual field examination revealed central or ceco-central scotoma in 17 eyes(48%) and other variable visual field defects. Visual evoked potential was abnormal in 89% of the examined eyes. Magnetic resonance imaging showed optic nerve enhancement in 48% and characteristic findings consistent with multiple sclerosis was seen in 6% of the examined subjects. This result suggests that the optic neuritis in Korea present with more papillitis than retrobulbar optic neuritis and multiple sclerosis is less commonly seen compared with previous reports of Caucasian optic neuritis.
Diagnosis ; Evoked Potentials, Visual ; Female ; Follow-Up Studies ; Humans ; Korea* ; Magnetic Resonance Imaging ; Male ; Multiple Sclerosis ; Optic Nerve ; Optic Neuritis* ; Papilledema ; Retrospective Studies ; Scotoma ; Visual Acuity ; Visual Fields

We performed treat the 41 eyes of rhegmatogenous retinal detachment to scleral encircling.The causes of retinal detachment were unidentifiable breaks (10 eyes), high myopia (8 eyes), pseudophakia or aphakia (8 eyes), giant tear (8 eyes)and multiple holes (7 eyes). Overall the reattachment ratewas 80.5% (33/41 eyes). The anatomic success rate was relatively high (85.7%)in eyes with giant tear, high myopia and multiple hole but relatively low in eyes with breaks unidentified (60%) or pseudophakic and aphakic retinal detachment (75%). Among those 33 eyes, functional success was achived in 27 eyes (81.8%). We achieved higher functional success rate in pseudophakia or aphakia, multiple hole and high myopia (over 83.3%) but low functional success rate in unidentifiable breaks (66.7%)and giant tear (71.4%). Our results suggest other treatments such as pars plana vitrectomy should be considered to treat eyes with retinal detachment of breaks unidentified, although scleral encircling has been used conventially.
Aphakia ; Myopia ; Pseudophakia ; Retinal Detachment* ; Retinaldehyde* ; Vitrectomy

The solitary fibrous tumor was a rare spindle cell tumor of adults that typically arised in the pleura, but also has been described in extrapleural sites.Recently, solitary fibrous tumors of the orbital soft tissue have been described. We confirmed a case of solitary fibrous tumor of lacrimal gland by histological and immunohistochemical examination in a 20-year-old female patient with left lateral upper eyelid mass.We report this case with literature review.
Adult ; Eyelids ; Female ; Humans ; Lacrimal Apparatus* ; Orbit ; Pleura ; Solitary Fibrous Tumors* ; Young Adult

The steatocystoma is a solitary or multiple cystic tumor, which usually occurs on the face, chest or axilla. To our knowledge, there has been no case report of steatocystoma in the orbit in Korea. We experienced a 22-year-old female patient with a steatocystoma in the orbit, which was diagnosed by histopathologic examination.
Axilla ; Female ; Humans ; Korea ; Orbit* ; Thorax ; Young Adult

PURPOSE: Paraquat (Gramoxone;1,1'dimethyl 4,4'-dipyridilium) is a toxic herbicide. It is ingested accidently or for the purpose of suicide in rural community. Having experienced four patients receiving donor corneas from the victims of Gramoxone poisoning, we report these cases with the review of the literature. METHODS: Four corneas donated by two males who died of Gramoxone intoxication were used in corneal transplantation of 4 patients. RESULTS: At postoperative 12 months, uncorrected visual acuity in each of the 3 patients was 0.1, 0.3 and 0.04, and each cornea maintained transparency. One patient had a retransplantation due to corneal epithelial cell defect and at postoperative 12 months, uncorrected visual acuity was 0.9.
Cornea ; Corneal Transplantation ; Epithelial Cells ; Humans ; Male ; Paraquat* ; Poisoning* ; Rural Population ; Suicide ; Tissue Donors* ; Visual Acuity