No abstract available.
Neurofibroma*

Kawasaki disease is an acute febrile illness frequently developed in infants and children. This disease may involve coronary arteries in 15- 25% of the patients and may progress to coronary aneurysms, ischemic cardiac diseases, and sudden cardiac death. Recently we experienced successful balloon angioplasty followed by coronary stenting in a 15-year old boy with unstable angina and severe coronary arterial occlusive disease secondary to Kawasaki disease. He was diagnosed as unstable angina by 24 hours Holter monitoring, treadmill exercise stress test, echocardiography, and Dipyridamole 99mTc-sestamibi scan. And coronary angiogram revealed severe multiple stenosis and aneurysmal changes due to Kawasaki disease. We successfully performed a percutaneous transluminal coronary angioplasty with stent implantation at left circumflex arterial occlusive lesion.
Adolescent ; Aneurysm ; Angina, Unstable ; Angioplasty, Balloon ; Angioplasty, Balloon, Coronary ; Arterial Occlusive Diseases ; Child ; Constriction, Pathologic ; Coronary Aneurysm ; Coronary Stenosis* ; Coronary Vessels* ; Death, Sudden, Cardiac ; Dipyridamole ; Echocardiography ; Electrocardiography, Ambulatory ; Exercise Test ; Heart Diseases ; Humans ; Infant ; Male* ; Mucocutaneous Lymph Node Syndrome* ; Stents* ; Technetium Tc 99m Sestamibi

Burkitt's lymphoma with a frankly leukemic picture is an extremely rare condition, and usually has a very acute course with a poor prognosis. The authors experienced two cases of Burkitt's lymphoma developed acute leukemia. The first case was 8 years-old boy who had rapidly growing large abdominal mass, which revealed typical Burkitt's lymphoma with characteristic "starrysky" pattern. The second case was 20 year old male who had not definite tumor mass. Their peripheral blood and bone marrow aspiration revealed acute leukemia with multiple vacuolated lymphoblast of Burkitt's type. We report these cases with brief review of literatures.
Male ; Humans

No abstract available.
Pelvic Exenteration*

No abstract available.
Pelvic Exenteration*

No abstract available.
Pelvic Exenteration*

BACKGROUND: Pemphigus is a chronic blistering disease of the skin and mucous membranes, with severe morbidity and occasional mortality. It is necessary to investigate the clinical features, treatment and long-term outcome of Korean patients with pemphigus as it is the most common and severe autoimmune bullous disease in Korea. OBJECTIVE: The purpose of this study was to evaluate the clinical features, treatment and prognosis of Korean patients with pemphigus. METHOD: A retrospective analysis was conducted on 124 pemphigus patients seen between 1987 and 2003 at Youngdong Severance Hospital. RESULTS: Out of 124 patients diagnosed with pemphigus during the study period, 62 patients had pemphigus vulgaris (PV), and 62 patients had pemphigus foliaceus (PF). For the 62 PV patients, the mean age of onset was 48.3 years, and the male to female ratio was 1: 1.7. For the 62 PF patients, the mean age of onset was 44.7 years, and the male to female ratio was 1.4: 1. Average initial dose of oral prednisolone was 30.2mg in PV patients and 19.9mg in PF. Fifty six (90%) patients with PV and 38 (61%) patients with PF received immunosuppressive agents. Partial remission was induced in 9.7%, 23.0%, 41.7%, and 75% of PV patients and in 12.9%, 19.0%, 13.6% and 50% of PF patients after 1, 3, 5, and 10 years of diagnosis, respectively. Five (8%) of each PV and PF patients died during the treatment period. CONCLUSION: The clinical manifestations and results of immunofluorescent studies on 124 Korean pemphigus patients were similar to those of previous studies. Contrast to previous studies, the PV to PF ratio was 1: 1, and a male preference was observed on PF. More studies are needed to improve the prognosis and reduce the complications in the treatment of pemphigus patients.
Age of Onset ; Blister ; Diagnosis ; Female ; Humans ; Immunosuppressive Agents ; Korea ; Male ; Mortality ; Mucous Membrane ; Pemphigus* ; Prednisolone ; Prognosis ; Retrospective Studies ; Skin

No abstract available.
Biliary Tract*

BACKGROUND: The use of prednisone in the treatment of myasthenia gravis (MG) has been required circumspection because of its tendency to produce exacerbations of weakness in the early stages of treatment, often requiring critical management. However, factors influencing the exacerbation has not been defined well. The purpose of this study was to evaluate the clinical factors predicting the exacerbation by prednisone in the early stage of treatment in MG. METHODS: Fifty five patients, first-ever prescribed high dose prednsone (40-80 mg) during hospitalization in Samsung Medical Center were included. Prednisone induced exacerbation was defined as significant exacerbation of objective neurologic signs of MG within 4 weeks after prednisone addition by utilizing Myasthnia gravis Severity Scale (MSS). We investigate the differences between the exacerbated and nonexacerbated groups in the clinical, laboratory and electrophysiological features. RESULTS: Twenty three patients (42%) experienced definite exacerbation after prednisone treatment. Old age, presence of bulbar symptom, and severe neurologic finding reflected by MSS score were significant predictors of prednisone induced exacerbation in multivariate logistic regression analysis. Higher prednisone dosage per body weight (Kg) was neither a significant predictor of exacerbation nor related with the early improvement in bivariate correlation. CONCLUSIONS: Prednisone induced exacerbation in MG is a frequent challenging problem to clinician. Clinicans should keep in mind the possibility of exacerbation of MG when prescribing prednisone especially, to old, bulbar dominant, severe and disable myasthenic patients.
Body Weight ; Hospitalization ; Humans ; Logistic Models ; Myasthenia Gravis* ; Neurologic Manifestations ; Prednisone

No abstract available.
Knee* ; Popliteal Artery*