Bladder exstrophy is one of the most profound genitourinary anomaly and it affects psychosocial development. Herein author reported a case of female bladder exstrophy in 10 month old baby repaired by primary closure of bladder exstrophy.
Bladder Exstrophy* ; Female* ; Humans ; Infant ; Urinary Bladder*

Primary closure of bladder exstrophy in a one-day-old-girl was performed with paraexstrophy skin flap and pubic bone approximation without osteotomy.
Bladder Exstrophy ; Female* ; Humans ; Infant, Newborn* ; Osteotomy ; Pubic Bone ; Skin

Bladder exstrophy is a rare condition with an incidence of between 1 in 10,000 and 1 in 50,000 live births and the male-to-female ratio ranges 2.3:1 to 6:1. The basic defect of bladder exstrophy is an abnormal overdevelopment of the cloacal membrane, preventing medial migration of the mesenchymal tissue and proper lower abdominal wall development. Although there are some recent successful reports of the one-stage repair of bladder exstrophy that involves complete primary repair of exstrophy and total disassembly of the epispadiac penis, staged repair still represents the most common operation for correction of this anomaly. A successful initial closure of the infant born with bladder exstrophy is the single most important determinant of continence in the staged repair of exstrophy patient. We report a case of bladder exstrophy with successful initial closure of bladder using posterior iliac osteotomy and paraexstrophy skin flap.
Abdominal Wall ; Bladder Exstrophy* ; Humans ; Incidence ; Infant ; Live Birth ; Male ; Membranes ; Osteotomy ; Penis ; Skin ; Urinary Bladder*

We report here the short-term results of 3 cases of cloacal and bladder exstrophy that underwent complete primary exstrophy repair. One case was diagnosed as bladder exstrophy and the others were diagnosed as cloacal exstrophy. Complete primary exstrophy repair for all 3 cases was carried out within 24 hours after birth. There was no wound dehiscence within the follow-up period of 12 months. The complete primary exstrophy repair with positioning the bladder neck and urethra in the deep pelvic cavity achieves a satisfactory short-term result.
Bladder Exstrophy* ; Cloaca ; Follow-Up Studies ; Neck ; Parturition ; Reconstructive Surgical Procedures ; Urethra ; Urinary Bladder* ; Wounds and Injuries

It is well known that there always exists danger of injury to the urinary tract associated with gynecologic disorders and treatments. Herein the authors describe two different rare cases: bilateral complete ligations of the lower ureters following total hysterectomy and herniated urinary bladder as exstrophy of the bladder through vesico-vaginal fistula caused by cauterization of the uterine prolapse for treatment.
Bladder Exstrophy ; Cautery ; Fistula ; Hysterectomy ; Ligation ; Ureter ; Urinary Bladder ; Urinary Tract ; Uterine Prolapse

Omphalocele-exstrophy-imperforate anus-spinal defects(OEIS Syndrome) is a single defect in early mesoderm, and its incidence is about one in 250,000. If was first described by Littre in 1709. The characteristics of this disorder is omphalocele, extrpohy of bladder, imperforate anus and spina bifida. There have been reports of longtime survival made possible by several operations, but for most cases normal life is impossible due to the deformities. We report a case of OEIS complex who had omphalocele, exstrophy of bladder, imperforate anus and spina bifida from birth.
Anus, Imperforate ; Bladder Exstrophy ; Congenital Abnormalities ; Hernia, Umbilical ; Incidence ; Mesoderm ; Parturition ; Spinal Dysraphism ; Urinary Bladder

Omphalocele-exstrophy-imperforate anus-spinal defects(OEIS Syndrome) is a single defect in early mesoderm, and its incidence is about one in 250,000. If was first described by Littre in 1709. The characteristics of this disorder is omphalocele, extrpohy of bladder, imperforate anus and spina bifida. There have been reports of longtime survival made possible by several operations, but for most cases normal life is impossible due to the deformities. We report a case of OEIS complex who had omphalocele, exstrophy of bladder, imperforate anus and spina bifida from birth.
Anus, Imperforate ; Bladder Exstrophy ; Congenital Abnormalities ; Hernia, Umbilical ; Incidence ; Mesoderm ; Parturition ; Spinal Dysraphism ; Urinary Bladder

Exstrophy of the bladder is a rare congenital anomaly with an incidence of about 1 per 50,000 newborns. The malignant potential of the exstrophied bladder mucosa is well known; 95% are adenocarcinomas, and 3% to 5% are squamous cell carcinomas. Most of the malignant tumors (60%) associated with an exstrophy of the bladder occur during the fourth and fifth decades of life. Of the remaining, about 20% each occur after 60 years and before 40 years. Here we present a case in which squamous cell carcinoma developed in an unrepaired exstrophy of the bladder. We present the management of the case and a brief review of the literature.
Adenocarcinoma ; Bladder Exstrophy ; Carcinoma, Squamous Cell ; Humans ; Incidence ; Infant, Newborn ; Mucous Membrane ; Urinary Bladder ; Urinary Bladder Neoplasms

The pathogenesis of bladder and cloacal exstrophy is an abnormal development of the cloacal membrane. The incidence of each is one in l0,000-50,000 and 200,000-400,000 live births. Male is more commonly affected than female. We experienced two cases of bladder exstrophy and one cloacal. First case was one-day-old girl who was referred to our department because of urine leakage through defected abdominal wall. We performed primary bladder closure with paraexstrophy skin flap urethroplasty, approximation and traction of pubis without osteotomy and application of hip-spica cast. The second was seven-day-old boy visited our department because of urine and stool leakage. We performed primary bladder closure, bilateral orchiectomy and ileostomy. He recurred bladder exstrophy due to infection of operation site. The third was twenty-day-old boy visited our department because of urine leakage. We recommended admission and treatment, but his parents refused further evaluation.
Abdominal Wall ; Bladder Exstrophy* ; Cloaca ; Female ; Humans ; Ileostomy ; Incidence ; Live Birth ; Male ; Membranes ; Orchiectomy ; Osteotomy ; Parents ; Skin ; Traction ; Urinary Bladder*

Bladder exstrophy is a rare congenital malformation in which the anterior wall of the bladder is absent, and the posterior wall is exposed. Because of the poor prognosis, prenatal diagnosis is important. We present a case of bladder exstophy which was presented as a solid mass in the lower part of the fetal abdomen instead of fluid-filled urinary bladder, and confirmed at autopsy after termination of pregnancy. To the best of our knowledge, this is the first report of bladder exstrophy prenatally diagnosed in the Korean literature.
Abdomen ; Autopsy ; Bladder Exstrophy* ; Diagnosis* ; Female ; Fetus ; Humans ; Pregnancy ; Pregnancy Trimester, Second* ; Pregnancy* ; Prenatal Diagnosis ; Prognosis ; Ultrasonography* ; Urinary Bladder* ; Urogenital System