【Objective】 To analyze the clinicopathological features of bladder urothelial carcinoma BUC in children and to share the experience of diagnosis and treatment. 【Methods】 The clinicopathological data, diagnosis and treatment process of a rare 9-year-old boy with BUC treated in the Second People’s Hospital of Kashgar were reported and the literature was reviewed. 【Results】 The main clinical symptom is hematuria. Both preoperative urinary ultrasound and CT urography (CTU) identified the tumor, which was then removed with transurethral holmium laser resection under general anesthesia. Postoperative pathology confirmed papillary urothelial neoplasm of low malignant potential (PUNLMP). Epirubicin hydrochloride instillation was administered, and no evidence of recurrence or progress was detected during the 3-month follow-up. 【Conclusion】 Bladder urothelial carcinoma in children is extremely rare.The most common symptom is hematuria, and there are no characteristic signs. Urinary ultrasound is the first choice for preoperative imaging, and transurethral resection of the carcinoma results in good recovery.There is no recommendable instillation, and patients need long-term postoperative follow-up.