This is a 1.5Kg female baby delivered in the department of Obstetrics and Gynecology of Severance Hospital with normal spontaneous vaginal delivery at 32 weeks gestation period. In delivery room they noticed eviceration of the entire liver, small intestine and stomach through an abdominal wall defect above umbilicus without a covering membrane. Umbilicus was normally inserted at the inferior margin of the abdominal wall defect. This anomaly was diagnosed as Gastroschisis after reviewing the literature. This is the first case report of Gastroschisis in Korea.
Abdominal Muscles/*abnormalities ; Female ; Human ; Infant, Newborn ; Intestine, Large/*abnormalities ; Intestine, Small/*abnormalities ; Liver/*abnormalities ; Stomach/*abnormalities

Cantrell's Pentalogy is a rare condition that consists of defects involving the abdominal wall, lower sternum, anterior diaphragm, pericardium, and heart. In the literature to date, pregnant women with Cantrell's Pentalogy have not been discussed. We performed successful vaginal delivery of a 23-yr-old nulliparous, primigravid woman who had been diagnosed with this condition. Diagnosis was based on cardiac catheterization, angiography, and echocardiogram, and abdominopelvic CT. Vaginal delivery may be an option for women with Cantrell's Pentalogy and may be attempted with caution.
Abdominal Muscles/abnormalities ; Abdominal Wall/abnormalities ; *Abnormalities, Multiple ; Diaphragm/abnormalities ; Echocardiography ; Female ; Humans ; Oligohydramnios/diagnosis ; Pregnancy ; *Pregnancy Complications ; Pregnancy Outcome ; Sternum/abnormalities ; Tomography, X-Ray Computed ; Young Adult

We have recently experienced a case of prune-belly syndrome, in 119/12-year-old male child with congenital defects of abdominal muscles, cryptorchidism, hydronephrosis, megacystis and spina bifida. Diagnosis was confirmed by EMG, IVP, retrograde cystogram, radiorenogram & renal scanning, and roentgenologic examinations. The patient in this report may be one of the most long-term survival case reported in korean literature.
Abdominal Muscles ; Child ; Congenital Abnormalities ; Cryptorchidism ; Diagnosis ; Humans ; Hydronephrosis ; Male ; Prune Belly Syndrome* ; Spinal Dysraphism

The author experienced a case of Prune belly syndrome, 7 week old male infant who presented with congenital defects of abdominal muscles, unilateral(Rt) undscended testis megacystitis and micrognathia.
Abdominal Muscles ; Congenital Abnormalities ; Humans ; Infant ; Male ; Prune Belly Syndrome* ; Testis

OBJECTIVETo sum up the methods repairing the congenital bladder exstrophy, and to evaluate the value of the abdominal fascial flap and the lower abdominal skin flap, the tensor fascia lata musculocutaneous flap treating the bladder exstrophy.

METHODSThe abdominal rectus sheath and the fascia flap of obliquus externus abdominal and the lower abdominal skin flap, or the tensor fascia lata musculocutaneous flap were used to repair the abdominal wall defection, meanwhile repair the epispadias. The maximum field of the musculocutaneous flaps was 8 cm x 10 cm.

RESULTS12 cases were cured. The bladder exstrophy and the abdominal wall defection were repaired very well. The musculus sphincter bladder neck was reconstructed. After the second operation, the cases could urinate under self-control. 2 skin flaps of 8 musculocutaneous flaps were necrosis and cured by skin grafting.

CONCLUSIONSUsing the abdominal fascial flap and the lower abdominal skin flap, or the tensor fascia lata musculocutaneous flap, is feasible for repairing the bladder exstrophy and the lower abdominal wall defection. The continuous of the musculus sphincter bladder were renewed, and then the patients could urinate under self-control. When the ischemia of the musculocutaneous flaps had occurred, the tensor fascial was survived well.

Abdominal Muscles ; Adolescent ; Adult ; Child ; Child, Preschool ; Fascia ; transplantation ; Female ; Humans ; Male ; Reconstructive Surgical Procedures ; methods ; Rectus Abdominis ; transplantation ; Surgical Flaps ; Urinary Bladder ; abnormalities ; Young Adult