No abstract available.
Ovotesticular Disorders of Sex Development*

No abstract available.
Ovotesticular Disorders of Sex Development*

Ovotesticular disorder of sexual differentiation (OT-DSD) is a rare condition defined by the presence of both testicular and ovarian elements in the same individual. Definitive diagnosis is made based on histological assessment of the gonad/s confirming both ovarian and testicular components. In this paper, we describe how a diagnosis of 46XX, OT-DSD was made in a 20-year-old individual with enlarged breasts and ambiguous genitalia. The initial impression was congenital adrenal hyperplasia (CAH) based on 46, XX karyotype and absence of testes on physical examination and imaging. However, biochemical tests were inconsistent with CAH, hence a more probable diagnosis of 46, XX OT-DSD was considered. The patient suffered from gender dysphoria and after extensive counseling, he decided to undergo gender-affirming surgery: laparoscopic excision of the left gonad, subtotal hysterectomy, bilateral mastectomy, and a masculinizing genitoplasty. Histopathology of the left gonad revealed an ovotestes which confirmed the diagnosis of 46, XX OT-DSD.
Ambiguous genitalia ; disorders of sex development ; intersex ; ovotesticular

True hermaphroditism is characterized by the coexistence of testicular and ovarian tissue. Authors experienced a case of true hermaphroditism which was confirmed an ovary in the left abdomen and testis in the right scrotum with a karyotype of 46, XX,47, XXY and report this case with the brief review of literatures.
Abdomen ; Female ; Karyotype* ; Ovary ; Ovotesticular Disorders of Sex Development* ; Scrotum ; Testis

True hermaphroditism is a rare disorder or sexual development in which both ovarian and testicular tissue exist in a same individual. Author experienced a case of true hermaphroditism in a 15 years old patient, reared as a male who had an ovotestis in the right side and ovary in the left, managed by resection of testicular tissue and feminine genitoplasty.
Adolescent ; Female ; Humans ; Male ; Ovary ; Ovotesticular Disorders of Sex Development* ; Sexual Development

Between January 1987 and February 1990, records of 5Z patients with 60 impalpable testes who had surgery were reviewed retrospectively regarding localization and management of the testes. Seven out of 60 testes turned out to be palpable by careful examination under anesthesia. Ultrasonogram detected 8 testes (5 intracanalicular and 3 preperitoneal) out of 25 testes. Laparoscopy provided and in planning the appropriate surgical approach in all 8 testes. Of the 47 testes found at surgery 19 were intraabdominal, 14 intracanalicular, 12 in preperitoneal and 1 located in superficial inguinal area. Also 13 vanished testes were confirmed during surgery examining blind end of spermatic vessels and vasa. Two patients with intersex ( true hermaphroditism and hernia uteri inguinalis) were presented as unilateral impalpable testes. 42 testes were brought down surgically utilizing regular orchiopexy in 26 testes, transabdominal orchiopexy in 8 testes, Fowler-Stephens orchiopexy in 7 testes and staged orchiopexy in 1 testis were done with acceptable results. transabdominal approach is recommended in cases of suspecting intraabdominal testis or intersex.
Anesthesia ; Hernia ; Humans ; Laparoscopy ; Orchiopexy ; Ovotesticular Disorders of Sex Development ; Retrospective Studies ; Testis* ; Ultrasonography ; Uterus

True hermaphroditism is a very rare congenital anomaly, in which both an ovary and a testis or a gonad with the histologic features of both(ovotestis) is present. So the external and internal genital organs are abnormally differentiated. We report 4 cases of true hermaphroditism with the review of the literatures.
Disorders of Sex Development ; Female ; Genitalia ; Gonads ; Ovary ; Ovotesticular Disorders of Sex Development* ; Testis

True hermaphroditism in which both ovarian and testicular tissues are present in same individual is a rare abnormality. Abnormal differentiation of external and internal genitalia is also observed. A total of 30O cases found in the literature by Niekerk, V.A. During exp1oratory surgery, testicular as well as ovarian tissues are found generally. Authors experienced one case of true hermaphroditism who had an ovotestis on the right gonad an ovary on the left with a karyotype of 46, XX and report this case with the review of literatures.
Disorders of Sex Development ; Female ; Genitalia ; Gonads ; Karyotype ; Ovary ; Ovotesticular Disorders of Sex Development*

True hermaphroditism represents the rarest of all intersex disorders. The condition is defined by the presence of both ovarian and testicular tissue in the same individual. True hermaphroditism is usually diagnosed during the newborn period in the course of evaluating ambiguous genitalia. We present an unusual case of a 15-year-old boy with phenotypically normal male genitalia and bilaterally descended ovotestis, who was seen for evalution of intermittent scrotal swelling and pain.
Adolescent ; Disorders of Sex Development ; Genitalia, Male ; Humans ; Infant, Newborn ; Male ; Ovotesticular Disorders of Sex Development*

We have proved the alternating type of true hermapbroditism by the microscopic evidence of both ovarian and testicular tissues. The sex was reassigned the male with concerning of sex of assignment and rearing. gender roles and orientation, the morphology of external genitalia and injurious psychological sequelae. We had then considerable effect in the use of Testosterone.
Disorders of Sex Development ; Gender Identity ; Genitalia ; Humans ; Male ; Ovotesticular Disorders of Sex Development* ; Testosterone