A 7-year-old well and healthy boy was hospitalized for the first time for severe respiratory distress. He was diagnosed with congenital cystic adenomatoid malformation (CCAM) and bronchopulmonary sequestration (BPS). CCAM and BPS are rare congenital pulmonary diseases and their presentation concurrently as a hybrid lesion is even rarer. CCAM is usually diagnosed prenatally however it may regress postnatally and the patient may be asymptomatic. BPS usually presents after birth or later in childhood with recurrent lung infections. We highlight this case of hybrid lesion of CCAM and BPS with an atypical clinical presentation which was lifesaving surgically with diagnosis made via radiographic imaging.
Bronchopulmonary Sequestration