2.Sturge-Weber-Syndrome with Extreme Ocular Manifestation and Rare Association of Upper Airway Angioma with Anticipated Difficult Airway
Hon Seng Wong ; Ropilah Abdul Rahman ; Swee Ying Choo ; Nurlia Yahya
The Medical Journal of Malaysia 2012;67(4):435-437
We report a rare case of an 18 year old girl with Sturge-
Weber syndrome, she had extensive facial port wine stains,
right bupthalmos and advanced glaucoma involving both
eyes. She underwent right eye glaucoma drainage device
surgery under general anaesthesia, and had a difficult
intubation due to extensive angiomatous like soft tissue
swelling at her upper airway. This report highlights the
importance of being aware of the need for continuous
follow-up in Sturge-Weber syndrome patients as this
syndrome can lead to blindness due to advance glaucoma
and the awareness of possible difficult intubation for this
group of patients.