Biliary atresia is one of the commonest causes of prolonged jaundice in neonate, whereas cystic biliary atresia is a rare form of biliary atresia with similar presentation, but a slightly different sonographic finding. Being able to differentiate them radiologically is important as the surgical management is different for these two diagnoses. An ultrasound examination was done for a 2-month-old baby girl with prolonged jaundice with the finding of a cyst along the portal triad, which raised the suspicion for cystic biliary atresia. The diagnosis was confirmed with intraoperative cholangiography (IOC) and Kasai procedure was done. The patient was well after the surgery with resolution of jaundice.

A 7-year-old well and healthy boy was hospitalized for the first time for severe respiratory distress. He was diagnosed with congenital cystic adenomatoid malformation (CCAM) and bronchopulmonary sequestration (BPS). CCAM and BPS are rare congenital pulmonary diseases and their presentation concurrently as a hybrid lesion is even rarer. CCAM is usually diagnosed prenatally however it may regress postnatally and the patient may be asymptomatic. BPS usually presents after birth or later in childhood with recurrent lung infections. We highlight this case of hybrid lesion of CCAM and BPS with an atypical clinical presentation which was lifesaving surgically with diagnosis made via radiographic imaging.
Bronchopulmonary Sequestration